See Section I.C.21. Factors influencing health status and contact with health services, Screening Appendix I Present on Admission Reporting Guidelines Introduction These guidelines are to be used as a supplement to the ICD-10-CM Official Guidelines for Coding and Reporting to facilitate the assignment of the Present on Admission (POA) indicator for each diagnosis and external cause of injury code reported on claim forms (UB-04 and 837 Institutional). These guidelines are not intended to replace any guidelines in the main body of the ICD-10-CM Official Guidelines for Coding and Reporting. The POA guidelines are not intended to provide guidance on when a condition should be coded, but rather, how to apply the POA indicator to the final set of diagnosis codes that have been assigned in accordance with Sections I, II, and III of the official coding guidelines. Subsequent to the assignment of the ICD-10-CM codes, the POA indicator should then be assigned to those conditions that have been coded. As stated in the Introduction to the ICD-10-CM Official Guidelines for Coding and Reporting, a joint effort between the healthcare provider and the coder is essential to achieve complete and accurate documentation, code assignment, and reporting of diagnoses and procedures. The importance of consistent, complete documentation in the medical record cannot be overemphasized. Medical record documentation from any provider involved in the care and treatment of the patient may be used to support the determination of whether a condition was present on admission or not. In the context of the official coding guidelines, the term “provider” means a physician or any qualified healthcare practitioner who is legally accountable for establishing the patient’s diagnosis. These guidelines are not a substitute for the provider’s clinical judgment as to the determination of whether a condition was/was not present on admission. The provider should be queried regarding issues related to the linking of signs/symptoms, timing of test results, and the timing of findings. Please see the CDC website for the detailed list of ICD-10-CM codes that do not require the use of a POA indicator (https://www.cdc.gov/nchs/icd/icd-10-cm/files.html). The codes and categories on this exempt list are for circumstances regarding the healthcare encounter or factors influencing health status that do not represent a current disease or injury or that describe conditions that are always present on admission. General Reporting Requirements All claims involving inpatient admissions to general acute care hospitals or other facilities that are subject to a law or regulation mandating collection of present on admission information. Present on admission is defined as present at the time the order for inpatient admission occurs -- conditions that develop during an outpatient encounter, including emergency department, observation, or outpatient surgery, are considered as present on admission. POA indicator is assigned to principal and secondary diagnoses (as defined in Section II of the Official Guidelines for Coding and Reporting) and the external cause of injury codes. Issues related to inconsistent, missing, conflicting or unclear documentation must still be resolved by the provider. If a condition would not be coded and reported based on UHDDS definitions and current official coding guidelines, then the POA indicator would not be reported. Reporting Options Y – Yes N – No U – Unknown W – Clinically undetermined Unreported/Not used – (Exempt from POA reporting) Reporting Definitions Y = present at the time of inpatient admission N = not present at the time of inpatient admission U = documentation is insufficient to determine if condition is present on admission W = provider is unable to clinically determine whether condition was present on admission or not Timeframe for POA Identification and Documentation There is no required timeframe as to when a provider (per the definition of “provider” used in these guidelines) must identify or document a condition to be present on admission. In some clinical situations, it may not be possible for a provider to make a definitive diagnosis (or a condition may not be recognized or reported by the patient) for a period of time after admission. In some cases, it may be several days before the provider arrives at a definitive diagnosis. This does not mean that the condition was not present on admission. Determination of whether the condition was present on admission or not will be based on the applicable POA guideline as identified in this document, or on the provider’s best clinical judgment. If at the time of code assignment the documentation is unclear as to whether a condition was present on admission or not, it is appropriate to query the provider for clarification. Assigning the POA Indicator Condition is on the “Exempt from Reporting” list Leave the “present on admission” field blank if the condition is on the list of ICD- 10-CM codes for which this field is not applicable. This is the only circumstance in which the field may be left blank. POA Explicitly Documented Assign Y for any condition the provider explicitly documents as being present on admission. Assign N for any condition the provider explicitly documents as not present at the time of admission. Conditions diagnosed prior to inpatient admission Assign “Y” for conditions that were diagnosed prior to admission (example: hypertension, diabetes mellitus, asthma) Conditions diagnosed during the admission but clearly present before admission Assign “Y” for conditions diagnosed during the admission that were clearly present but not diagnosed until after admission occurred. Diagnoses subsequently confirmed after admission are considered present on admission if at the time of admission they are documented as suspected, possible, rule out, differential diagnosis, or constitute an underlying cause of a symptom that is present at the time of admission. Condition develops during outpatient encounter prior to inpatient admission Assign Y for any condition that develops during an outpatient encounter prior to a written order for inpatient admission. Documentation does not indicate whether condition was present on admission Assign “U” when the medical record documentation is unclear as to whether the condition was present on admission. “U” should not be routinely assigned and used only in very limited circumstances. Coders are encouraged to query the providers when the documentation is unclear. Documentation states that it cannot be determined whether the condition was or was not present on admission Assign “W” when the medical record documentation indicates that it cannot be clinically determined whether or not the condition was present on admission. Chronic condition with acute exacerbation during the admission If a single code identifies both the chronic condition and the acute exacerbation, see POA guidelines pertaining to codes that contain multiple clinical concepts. If a single code only identifies the chronic condition and not the acute exacerbation (e.g., acute exacerbation of chronic leukemia), assign “Y.” Conditions documented as possible, probable, suspected, or rule out at the time of discharge If the final diagnosis contains a possible, probable, suspected, or rule out diagnosis, and this diagnosis was based on signs, symptoms or clinical findings suspected at the time of inpatient admission, assign “Y.” If the final diagnosis contains a possible, probable, suspected, or rule out diagnosis, and this diagnosis was based on signs, symptoms or clinical findings that were not present on admission, assign “N”. Conditions documented as impending or threatened at the time of discharge If the final diagnosis contains an impending or threatened diagnosis, and this diagnosis is based on symptoms or clinical findings that were present on admission, assign “Y”. If the final diagnosis contains an impending or threatened diagnosis, and this diagnosis is based on symptoms or clinical findings that were not present on admission, assign “N”. Acute and Chronic Conditions Assign “Y” for acute conditions that are present at time of admission and N for acute conditions that are not present at time of admission. Assign “Y” for chronic conditions, even though the condition may not be diagnosed until after admission. If a single code identifies both an acute and chronic condition, see the POA guidelines for codes that contain multiple clinical concepts. Codes That Contain Multiple Clinical Concepts Assign “N” if at least one of the clinical concepts included in the code was not present on admission (e.g., COPD with acute exacerbation and the exacerbation was not present on admission; gastric ulcer that does not start bleeding until after admission; asthma patient develops status asthmaticus after admission). Assign “Y” if all of the clinical concepts included in the code were present on admission (e.g., duodenal ulcer that perforates prior to admission). For infection codes that include the causal organism, assign “Y” if the infection (or signs of the infection) were present on admission, even though the culture results may not be known until after admission (e.g., patient is admitted with pneumonia and the provider documents Pseudomonas as the causal organism a few days later). Same Diagnosis Code for Two or More Conditions When the same ICD-10-CM diagnosis code applies to two or more conditions during the same encounter (e.g., two separate conditions classified to the same ICD-10-CM diagnosis code): Assign “Y” if all conditions represented by the single ICD-10-CM code were present on admission (e.g., bilateral unspecified age-related cataracts). Assign “N” if any of the conditions represented by the single ICD-10-CM code was not present on admission (e.g. traumatic secondary and recurrent hemorrhage and seroma is assigned to a single code T79.2, but only one of the conditions was present on admission). Obstetrical conditions Whether or not the patient delivers during the current hospitalization does not affect assignment of the POA indicator. The determining factor for POA assignment is whether the pregnancy complication or obstetrical condition described by the code was present at the time of admission or not. If the pregnancy complication or obstetrical condition was present on admission (e.g., patient admitted in preterm labor), assign “Y”. If the pregnancy complication or obstetrical condition was not present on admission (e.g., 2 degree laceration during delivery, postpartum hemorrhage that occurred during current hospitalization, fetal distress develops after admission), assign “N”. If the obstetrical code includes more than one diagnosis and any of the diagnoses identified by the code were not present on admission assign “N”. (e.g., Category O11, Pre-existing hypertension with pre-eclampsia) Perinatal conditions Newborns are not considered to be admitted until after birth. Therefore, any condition present at birth or that developed in utero is considered present at admission and should be assigned “Y”. This includes conditions that occur during delivery (e.g., injury during delivery, meconium aspiration, exposure to streptococcus B in the vaginal canal). Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission. External cause of injury codes Assign “Y” for any external cause code representing an external cause of morbidity that occurred prior to inpatient admission (e.g., patient fell out of bed at home, patient fell out of bed in emergency room prior to admission) Assign “N” for any external cause code representing an external cause of morbidity that occurred during inpatient hospitalization (e.g., patient fell out of hospital bed during hospital stay, patient experienced an adverse reaction to a medication administered after inpatient admission).
Q75.4
BookmarkMandibulofacial dysostosis
Filed alongside this entry 777
under Syndrome
- 4H G11.5
- 5q minus NOS D46.C
- 22q13.3 deletion Q93.52
- 48,XXXX Q97.1
- 49,XXXXX Q97.1
- abnormal innervation H02.519
- abstinence, neonatal P96.1
- acid pulmonary aspiration, obstetric O74.0
- activated phosphoinositide 3-kinase delta syndrome [APDS] D81.82
- acute abdominal R10.0
- acute respiratory distress (adult) (child) J80
- Adair-Dighton Q78.0
- Adams-Stokes (-Morgagni) I45.9
- adiposogenital E23.6
- adrenogenital E25.9
- afferent loop NEC K91.89
- Aicardi-Goutières E79.81
- Alagille (-Watson) Q44.71
- Alder's D72.0
- Aldrich (-Wiskott) D82.0
- alien hand R41.4
- Alpha-gal Z91.014
- Alport Q87.81
- alveolar hypoventilation E66.2
- alveolocapillary block J84.10
- amyostatic (Wilson's disease) E83.01
- androgen insensitivity E34.50
- androgen resistance E34.50
- Angelman Q93.51
- ankyloglossia superior Q38.1
- antibody deficiency D80.9
- anticardiolipin (-antibody) D68.61
- antidepressant discontinuation T43.205
- antiphospholipid (-antibody) D68.61
- aortomesenteric duodenum occlusion K31.5
- apical ballooning (transient left ventricular) I51.81
- arcuate ligament I77.4
- argentaffin, argintaffinoma E34.09
- Arrillaga-Ayerza I27.0
- arterial tortuosity Q87.82
- arteriovenous steal T82.898
- Asherman's N85.6
- ataxia-telangiectasia G11.3
- auriculotemporal G50.8
- autoerythrocyte sensitization (Gardner-Diamond) D69.2
- autoimmune polyglandular E31.0
- autoimmune lymphoproliferative [ALPS] D89.82
- autoinflammatory M04.9
- Avellis' G46.8
- Axenfeld-Rieger Q13.81
- Ayerza (-Arrillaga) I27.0
- Babinski-Nageotte G83.89
- Bakwin-Krida Q78.5
- Bardet-Biedl Q87.83
- bare lymphocyte D81.6
- Barré-Guillain G61.0
- Barré-Liéou M53.0
- Barsony-Polgar K22.4
- Barsony-Teschendorf K22.4
- Barth E78.71
- Bartter's E26.81
- basal cell nevus Q87.89
- Basedow's E05.00
- basilar artery G45.0
- Batten-Steinert G71.11
- Beals Q87.40
- Beau's I51.5
- Beck's I65.8
- Benedikt's G46.3
- Béquez César (-Steinbrinck-Chédiak-Higashi) E70.330
- Berardinelli-Siep E88.12
- big spleen D73.1
- bilateral polycystic ovarian E28.2
- Birt-Hogg-Dube syndrome Q87.89
- Björck (-Thorsen) E34.09
- Blackfan-Diamond D61.01
- Blau M04.8
- blind loop K90.2
- blue sclera Q78.0
- blue toe I75.02
- Boder-Sedgewick G11.3
- Boerhaave's K22.3
- Borjeson Forssman Lehmann Q89.89
- Bouillaud's I01.9
- Bourneville (-Pringle) Q85.1
- Bouveret (-Hoffman) I47.9
- brachial plexus G54.0
- bradycardia-tachycardia I49.5
- brain (nonpsychotic) F09
- brain stem stroke G46.3
- Brandt's (acrodermatitis enteropathica) E83.2
- BRCA1-cancer predisposition QA1.790
- BRCA2-cancer predisposition QA1.791
- broad ligament laceration N83.8
- Brock's J98.11
- bronchiolitis obliterans J44.81
- bronze baby P83.88
- Brown-Sequard G83.81
- Brugada I49.81
- bubbly lung P27.0
- Buchem's M85.2
- Budd-Chiari I82.0
- bulbar (progressive) G12.22
- Bürger-Grütz E78.3
- Burke's K86.89
- Burnett's (milk-alkali) E83.52
- burning feet E53.9
- Bywaters' T79.5
- Call-Fleming I67.841
- cannabinoid hyperemesis R11.16
- cannabis hyperemesis R11.16
- carbohydrate-deficient glycoprotein (CDGS) E77.8
- carcinogenic thrombophlebitis I82.1
- carcinoid E34.00
- cardiac asthma I50.1
- cardiacos negros I27.0
- cardiofaciocutaneous Q87.89
- cardiopulmonary-obesity E66.2
- cardiorespiratory distress (idiopathic) , newborn P22.0
- carpal tunnel G56.0
- Cassidy (-Scholte) E34.09
- cat cry Q93.4
- cat eye Q92.8
- cauda equina G83.4
- celiac K90.0
- central pain G89.0
- cervical (root) M53.1
- cervicobrachial (diffuse) M53.1
- cervicocranial M53.0
- cervicodorsal outlet G54.2
- cervicothoracic outlet G54.0
- Céstan (-Raymond) I65.8
- Charcot's (angina cruris) (intermittent claudication) I73.9
- Charcot-Weiss-Baker G90.09
- CHARGE Q89.89
- Chédiak-Higashi (-Steinbrinck) E70.330
- chest wall R07.1
- Chiari's (hepatic vein thrombosis) I82.0
- Chilaiditi's Q43.3
- chondrocostal junction M94.0
- chondroectodermal dysplasia Q77.6
- chromosome 4 short arm deletion Q93.3
- chromosome 5 short arm deletion Q93.4
- Churg-Strauss M30.1
- Clarke-Hadfield K86.89
- Clerambault's automatism G93.89
- clinically isolated G37.9
- Clouston's (hidrotic ectodermal dysplasia) Q82.4
- clumsiness, clumsy child F82
- cluster headache G44.009
- Coffin-Lowry Q89.89
- cold injury (newborn) P80.0
- combined immunity deficiency D81.9
- compartment (deep) (posterior) (traumatic) T79.A0
- compression T79.5
- concussion F07.81
- congestion-fibrosis (pelvic) , female N94.89
- congestive dysmenorrhea N94.6
- Conn's E26.01
- connective tissue M35.9
- conus medullaris G95.81
- Costen's (complex) M26.69
- costochondral junction M94.0
- costoclavicular G54.0
- costovertebral E22.0
- craniovertebral M53.0
- cri-du-chat Q93.4
- crib death R99
- croup J05.0
- crush T79.5
- CTNNB1 Q87.88
- Curschmann (-Batten) (-Steinert) G71.11
- Cushing's E24.9
- cryopyrin-associated periodic M04.2
- cryptophthalmos Q87.0
- cystic duct stump K91.5
- cytokine release D89.839
- Dana-Putnam D51.0
- Danbolt (-Cross) (acrodermatitis enteropathica) E83.2
- Dandy-Walker Q03.1
- Danlos' Q79.60
- Degos' I77.89
- Déjérine-Roussy G89.0
- delayed sleep phase G47.21
- demyelinating G37.9
- depersonalization (-derealization) F48.1
- De Quervain E34.51
- de Toni-Fanconi (-Debré) E72.09
- de Vivo syndrome E74.810
- diabetes mellitus in newborn infant P70.2
- dialysis associated steal T82.898
- Diamond-Blackfan D61.01
- Diamond-Gardener D69.2
- DIC (diffuse or disseminated intravascular coagulopathy) D65
- di George's D82.1
- Dighton's Q78.0
- disequilibrium E87.8
- Döhle body-panmyelopathic D72.0
- dorsolateral medullary G46.4
- double athetosis G80.3
- Down Q90.9
- Dravet (intractable) G40.834
- Dresbach's (elliptocytosis) D58.1
- DRESS (drug rash with eosinophilia and systemic symptoms) D72.12
- Dressler's (postmyocardial infarction) I24.1
- drug rash with eosinophilia and systemic symptoms (DRESS) D72.12
- drug withdrawal, infant of dependent mother P96.1
- dry eye H04.12
- dumping (postgastrectomy) K91.1
- Dupré's (meningism) R29.1
- dysmetabolic X E88.810
- dyspraxia, developmental F82
- Eagle-Barrett Q79.4
- Ebstein's Q22.5
- ectopic ACTH E24.3
- eczema-thrombocytopenia D82.0
- Eddowes' Q78.0
- effort (psychogenic) F45.8
- Eisenmenger's I27.83
- Ehlers-Danlos Q79.60
- Ekman's Q78.0
- electric feet E53.8
- Ellis-van Creveld Q77.6
- empty nest Z60.0
- endocrine-hypertensive E27.0
- eosinophilia-myalgia M35.89
- Erdheim-Chester (ECD) E88.89
- Erdheim's E22.0
- erythrocyte fragmentation D59.4
- Evans D69.41
- exhaustion F48.8
- extrapyramidal G25.9
- eyelid-malar-mandible Q87.0
- Faber's D50.9
- facet M47.89
- facet joint M47.819
- facial pain, paroxysmal G50.0
- Fallot's Q21.3
- familial cold autoinflammatory M04.2
- familial eczema-thrombocytopenia (Wiskott-Aldrich) D82.0
- Fanconi (-de Toni) (-Debré) E72.09
- faulty bowel habit K59.39
- Feil-Klippel (brevicollis) Q76.1
- fertile eunuch E23.0
- Fiedler's I40.1
- first arch Q87.0
- fish odor E72.89
- Fisher's G61.0
- Fitz's K85.80
- Flajani (-Basedow) E05.00
- flush E34.09
- Foix-Alajouanine G95.19
- Fong's Q87.2
- food protein-induced enterocolitis (FPIES) K52.21
- foramen magnum G93.5
- Foster-Kennedy H47.14
- Foville's (peduncular) G46.3
- FOXG1 QA0.0151
- fragile X Q99.2
- Franceschetti Q75.4
- Friderichsen-Waterhouse A39.1
- Froin's G95.89
- frontal lobe F07.0
- Fukuhara E88.49
- Gaisböck's D75.1
- ganglion (basal ganglia brain) G25.9
- Gardner-Diamond D69.2
- gastrojejunal loop obstruction K91.89
- Gee-Herter-Heubner K90.0
- Gelineau's G47.419
- genito-anorectal A55
- Gerstmann-Sträussler-Scheinker (GSS) A81.82
- Gianotti-Crosti L44.4
- giant platelet (Bernard-Soulier) D69.19
- Gilles de la Tourette's F95.2
- Glass Q87.89
- Gleich's D72.118
- goiter-deafness E07.1
- Goldberg Q89.89
- Goldberg-Maxwell E34.51
- Good's D83.8
- Gopalan's (burning feet) E53.8
- Gorlin's Q87.89
- Gougerot-Blum L81.7
- Gouley's I31.1
- Gower's R55
- gray or grey (newborn) P93.0
- Gubler-Millard G46.3
- Guillain-Barré (-Strohl) G61.0
- Gulf war T75.830
- gustatory sweating G50.8
- Hadfield-Clarke K86.89
- Hamman's J98.19
- hand-foot L27.1
- hand-shoulder G90.89
- hantavirus (cardio)-pulmonary (HPS) (HCPS) B33.4
- Hao-Fountain (HAFOUS) Q87.87
- happy puppet Q93.51
- Harada's H30.81
- Hayem-Faber D50.9
- headache NEC G44.89
- Heberden's I20.89
- Hedinger's E34.01
- Hegglin's D72.0
- HELLP (hemolysis, elevated liver enzymes and low platelet count) O14.2
- hemolytic-uremic D59.30
- hemophagocytic, infection-associated D76.2
- Henoch-Schönlein D69.0
- hepatic flexure K59.89
- hepatopulmonary K76.81
- hepatorenal K76.7
- hepatourologic K76.7
- hereditary alpha tryptasemia D89.44
- Herter (-Gee) (nontropical sprue) K90.0
- Heubner-Herter K90.0
- Heyd's K76.7
- Hilger's G90.09
- histiocytic D76.3
- histiocytosis NEC D76.3
- HIV infection, acute B20
- Hoffmann-Werdnig G12.0
- Hollander-Simons E88.19
- Hoppe-Goldflam G70.00
- Horner's G90.2
- hungry bone E83.81
- hunterian glossitis D51.0
- Hunt's (herpetic geniculate ganglionitis) (neuralgia) B02.21
- Hutchinson's triad A50.53
- hyperabduction G54.0
- hyperammonemia-hyperornithinemia-homocitrullinemia E72.4
- hypereosinophilic (HES) D72.119
- hyperimmunoglobulin D M04.1
- hyperimmunoglobulin E (IgE) D82.4
- hyperkalemic E87.5
- hypermobility M35.7
- hypernatremia E87.0
- hyperosmolarity (see also, Diabetes, by type, with hyperosmolarity) E87.0
- hyperperfusion G97.82
- hypersplenic D73.1
- hypertransfusion, newborn P61.1
- hyperventilation F45.8
- hypoglycemic (familial) (neonatal) E16.2
- hypokalemic E87.6
- hyponatremic E87.1
- hypopituitarism E23.0
- hypoplastic left-heart Q23.4
- hypopotassemia E87.6
- hyposmolality E87.1
- hypotension, maternal O26.5
- hypothenar hammer I73.89
- hypoventilation, obesity (OHS) E66.2
- ICF (intravascular coagulation-fibrinolysis) D65
- iliotibial band M76.3
- immobility, immobilization (paraplegic) M62.3
- immune effector cell-associated neurotoxicity (ICANS) G92.00
- immune reconstitution D89.3
- immune reconstitution inflammatory [IRIS] D89.3
- immunity deficiency, combined D81.9
- impending coronary I20.0
- impingement, shoulder M75.4
- inappropriate secretion of antidiuretic hormone E22.2
- infantilism (pituitary) E23.0
- inferior vena cava I87.1
- inherited neoplasm predisposition syndrome of multiple systems, specified NEC QA1.798
- inspissated bile (newborn) P59.1
- institutional (childhood) F94.2
- insufficient sleep F51.12
- intermediate coronary (artery) I20.0
- intravascular coagulation-fibrinolysis (ICF) D65
- iodine-deficiency, congenital E00.9
- IRDS (idiopathic respiratory distress, newborn) P22.0
- IVC (intravascular coagulopathy) D65
- Ivemark's Q89.01
- Jackson's G83.89
- jaw-winking Q07.8
- Jervell-Lange-Nielsen I45.81
- jet lag G47.25
- Job's D71.8
- Joseph-Diamond-Blackfan D61.01
- jugular foramen G52.7
- Kabuki (type 1, due to KMT2D mutation) (type 2, due to KDM6A mutation) Q89.81
- Kanner's (autism) F84.0
- Kartagener's Q89.3
- Kelly's D50.1
- Kleefstra Q87.86
- Klein (e) -Levine G47.13
- Klippel-Feil (brevicollis) Q76.1
- König's K59.89
- Korsakoff (-Wernicke) (nonalcoholic) F04
- Kostmann's D70.0
- Krabbe's congenital muscle hypoplasia Q79.8
- lacunar NEC G46.7
- Lambert-Eaton G70.80
- Larsen's Q74.8
- Lassueur Graham-Little Piccardi L66.19
- Launois' E22.0
- Laurence-Moon Q87.84
- Lawrence E88.12
- Lemierre I80.8
- Lennox-Gastaut G40.812
- lenticular, progressive E83.01
- Leopold-Levi's E05.90
- Lev's I44.2
- Li-Fraumeni QA1.792
- Lichtheim's D51.0
- Lightwood's N25.89
- Lignac (de Toni) (-Fanconi) (-Debré) E72.09
- Likoff's I20.89
- limbic epilepsy personality F07.0
- liver-kidney K76.7
- lobotomy F07.0
- Loeys-Dietz Q87.A
- Löffler's J82.89
- long arm 18 or 21 deletion Q93.89
- long QT I45.81
- Louis-Barré G11.3
- lower radicular, newborn (birth injury) P14.8
- Luetscher's (dehydration) E86.0
- Lupus anticoagulant D68.62
- Lutembacher's Q21.19
- Lynch (due to EPCAM) (due to MLH1) (due to MSH2) (due to MSH6) (due to PMS2) QA1.71
- macrophage activation D76.1
- magnesium-deficiency R29.0
- Majeed M04.8
- Mal de Debarquement R42
- malabsorption K90.9
- Mallory-Weiss K22.6
- mandibulofacial dysostosis Q75.4
- maple-syrup-urine E71.0
- Marable's I77.4
- Marfan Q87.40
- Marie's (acromegaly) E22.0
- May (-Hegglin) D72.0
- McArdle (-Schmidt) (-Pearson) E74.04
- McQuarrie's E16.2
- meconium plug (newborn) P76.0
- MED13L (mediator complex subunit 13L) Q87.85
- median arcuate ligament I77.4
- mediator complex subunit 13L (MED13L) Q87.85
- Meekeren-Ehlers-Danlos Q79.6
- megavitamin-B6 E67.2
- Meige G24.4
- MELAS E88.41
- Mendelson's O74.0
- MERRF (myoclonic epilepsy associated with ragged-red fibers) E88.42
- metabolic E88.810
- metastatic carcinoid E34.00
- micrognathia-glossoptosis Q87.0
- midbrain NEC G93.89
- middle lobe (lung) J98.19
- middle radicular G54.0
- migraine G43.909
- Mikulicz' K11.8
- milk-alkali E83.52
- Millard-Gubler G46.3
- Miller-Dieker Q93.88
- Miller-Fisher G61.0
- Minkowski-Chauffard D58.0
- Mirizzi's K83.1
- MNGIE (Mitochondrial Neurogastrointestinal Encephalopathy) E88.49
- monofixation H50.42
- Morel-Moore M85.2
- Morel-Morgagni M85.2
- Morgagni (-Morel) (-Stewart) M85.2
- Morgagni-Adams-Stokes I45.9
- Muckle-Wells M04.2
- mucocutaneous lymph node (acute febrile) (MCLS) M30.3
- multisystem inflammatory (in adults) (in children) M35.81
- Mounier-Kuhn Q32.4
- myasthenic G70.9
- myelodysplastic D46.9
- myeloid hypereosinophilic D72.118
- myelopathic pain G89.0
- myeloproliferative (chronic) D47.1
- myofascial pain M79.18
- Naffziger's G54.0
- nail patella Q87.2
- NARP (Neuropathy, Ataxia and Retinitis pigmentosa) E88.49
- neonatal abstinence P96.1
- nephrotic (congenital) N04.9
- neurologic neglect R41.4
- Nezelof's D81.4
- Niikawa-Kuroki Q89.81
- Nonne-Milroy-Meige Q82.0
- Nothnagel's vasomotor acroparesthesia I73.89
- obesity hypoventilation (OHS) E66.2
- oculomotor H51.9
- Ogilvie K59.81
- Oliver-McFarlane Q87.89
- oral allergy T78.19
- oral-facial-digital Q87.0
- Ormond's N13.5
- oro-facial-digital Q87.0
- os trigonum Q68.8
- Osler-Weber-Rendu I78.0
- osteoporosis-osteomalacia M83.8
- Osterreicher-Turner Q87.2
- oto-palatal-digital Q87.0
- outlet (thoracic) G54.0
- Owren's D68.2
- Paget-Schroetter I82.890
- paralytic G83.9
- Parinaud's H51.0
- paroxysmal facial pain G50.0
- Parry's E05.00
- Parsonage (-Aldren) -Turner G54.5
- patella clunk M25.86
- Paterson (-Brown) (-Kelly) D50.1
- pectoral girdle I77.89
- pectoralis minor I77.89
- pediatric acute-onset neuropsychiatric (PANS) D89.89
- pediatric autoimmune neuropsychiatric disorders associated with streptococcal infections (PANDAS) D89.89
- pediatric inflammatory multisystem M35.81
- Pelger-Huet D72.0
- pellagra-cerebellar ataxia-renal aminoaciduria E72.02
- pellagroid E52
- pelvic congestion-fibrosis, female N94.89
- penta X Q97.1
- perabduction I77.89
- periodic fever M04.1
- periodic fever, aphthous stomatitis, pharyngitis, and adenopathy [PFAPA] M04.8
- periurethral fibrosis N13.5
- Peutz-Jeghers Q85.89
- phantom limb (without pain) G54.7
- pharyngeal pouch D82.1
- Phelan-McDermid Q93.52
- Pickwickian E66.2
- PIE (pulmonary infiltration with eosinophilia) J82.89
- pigmentary pallidal degeneration (progressive) G23.0
- pineal E34.8
- pituitary E22.0
- plantar fascia M72.2
- plateau iris (post-iridectomy) (postprocedural) H21.82
- Plummer-Vinson D50.1
- pluricarential of infancy E40
- plurideficiency E40
- pluriglandular (compensatory) E31.8
- pneumatic hammer T75.21
- polyangiitis overlap M30.8
- polycarential of infancy E40
- polyglandular E31.8
- polysplenia Q89.09
- pontine NEC G93.89
- postbacterial fatigue G93.39
- postcardiotomy I97.0
- postcholecystectomy K91.5
- postcommissurotomy I97.0
- postconcussional F07.81
- postcontusional F07.81
- post-COVID (-19) U09.9
- postencephalitic F07.89
- post endometrial ablation N99.85
- post-polypectomy coagulation K91.89
- postgastrectomy (dumping) K91.1
- postgastric surgery K91.1
- postinfarction I24.1
- postinfectious fatigue G93.39
- postlaminectomy NEC M96.1
- postleukotomy F07.0
- postmastectomy lymphedema I97.2
- postmyocardial infarction I24.1
- postoperative NEC T81.9
- postpartum panhypopituitary (Sheehan) E23.0
- postpolio (myelitic) G14
- postthrombotic I87.009
- postvagotomy K91.1
- postvalvulotomy I97.0
- postviral NEC G93.31
- Potain's K31.0
- potassium intoxication E87.5
- Prader-Willi Q87.11
- Prader-Willi-like Q87.19
- precerebral artery (multiple) (bilateral) G45.2
- preinfarction I20.0
- preleukemic D46.9
- premature senility E34.8
- premenstrual dysphoric F32.81
- premenstrual tension N94.3
- Prinzmetal-Massumi R07.1
- prune belly Q79.4
- pseudoparalytica G70.00
- pseudo -Turner's Q87.19
- psycho-organic (nonpsychotic severity) F07.9
- PTEN (hamartoma) tumor Q85.81
- Putnam-Dana D51.0
- pyogenic arthritis, pyoderma gangrenosum, and acne [PAPA] M04.8
- pyramidopallidonigral G20.C
- QT interval prolongation I45.81
- rapid time-zone change G47.25
- Rasmussen G04.81
- Raymond (-Céstan) I65.8
- Raynaud's I73.00
- RDS (respiratory distress syndrome, newborn) P22.0
- reactive airways dysfunction J68.3
- Refsum's G60.1
- Reifenstein E34.52
- Rendu-Osler-Weber I78.0
- residual ovary N99.83
- resistant ovary E28.39
- restless legs G25.81
- restrictive allograft J4A.0
- retinoblastoma (familial) C69.2
- retroperitoneal fibrosis K68.2
- retroviral seroconversion (acute) Z21
- Reye's G93.7
- Ridley's I50.1
- Romano-Ward (prolonged QT interval) I45.81
- rotator cuff, shoulder M75.10
- rubella (congenital) P35.0
- Ruvalcaba-Myhre-Smith E71.440
- Rytand-Lipsitch I44.2
- salt-losing N28.89
- SATB2-associated Q87.89
- Scaglietti-Dagnini E22.0
- scalenus anticus (anterior) G54.0
- scapuloperoneal G71.09
- schizophrenic, of childhood NEC F20.9
- Schnitzler D47.2
- Scholte's E34.09
- Schroeder's E27.0
- Schüller-Christian C96.5
- Schwachman (-Diamond) D61.02
- Schwartz (-Jampel) G71.13
- Schwartz-Bartter E22.2
- scimitar Q26.8
- sclerocystic ovary E28.2
- Seitelberger's G31.89
- septicemic adrenal hemorrhage A39.1
- seroconversion, retroviral (acute) Z21
- serotonin G90.81
- serous meningitis G93.2
- severe acute respiratory (SARS) J12.81
- shaken infant T74.4
- shock (traumatic) T79.4
- shock-lung J80
- Shwachman (-Diamond) D61.02
- sick-euthyroid E07.81
- sideropenic D50.1
- Siemens' ectodermal dysplasia Q82.4
- Silfversköld's Q78.9
- Simons' E88.11
- sinus tarsi M25.57
- sinusitis-bronchiectasis-situs inversus Q89.3
- Sipple's E31.22
- sirenomelia Q87.2
- Sjögren M35.00
- Slocumb's E27.0
- slow flow, coronary I20.89
- Sluder's G44.89
- Smith-Magenis Q93.88
- Sneddon-Wilkinson L13.1
- Snyder-Robinson Q87.89
- Soto's Q87.3
- South African cardiomyopathy I42.89
- Spen's I45.9
- Spurway's Q78.0
- staphylococcal scalded skin L00
- Stein-Leventhal E28.2
- Stein's E28.2
- Stevens-Johnson syndrome L51.1
- Stewart-Morel M85.2
- Stickler Q89.89
- stiff baby Q89.89
- stiff man G25.82
- Stokes (-Adams) I45.9
- stone heart I50.1
- straight back, congenital Q76.49
- Sturge-Weber (-Dimitri) Q85.89
- subclavian steal G45.8
- subcoracoid-pectoralis minor G54.0
- subcostal nerve compression I77.89
- subphrenic interposition Q43.3
- suprarenal cortical E27.0
- supraspinatus M75.10
- Susac G93.49
- swallowed blood P78.2
- sweat retention L74.0
- Swyer Q99.1
- Symond's G93.2
- systemic inflammatory response (SIRS), of non-infectious origin (without organ dysfunction) R65.10
- tachycardia-bradycardia I49.5
- takotsubo I51.81
- TAR (thrombocytopenia with absent radius) Q87.2
- tarsal tunnel G57.5
- teething K00.7
- tegmental G93.89
- telangiectasic-pigmentation-cataract Q82.8
- temporomandibular joint-pain-dysfunction M26.62
- Terry's H44.2
- testicular feminization E34.51
- thalamic pain (hyperesthetic) G89.0
- thoracic outlet (compression) G54.0
- Thorson-Björck E34.09
- thrombocytopenia with absent radius (TAR) Q87.2
- thrombosis with thrombocytopenia D75.84
- thyroid-adrenocortical insufficiency E31.0
- Tietze's M94.0
- time-zone (rapid) G47.25
- Toni-Fanconi E72.09
- Touraine's Q79.8
- toxic shock A48.3
- transient left ventricular apical ballooning I51.81
- traumatic vasospastic T75.22
- Treacher Collins Q75.4
- triple X, female Q97.0
- trisomy Q92.9
- tropical wet feet T69.02
- Trousseau's I82.1
- tumor lysis (following antineoplastic chemotherapy) (spontaneous) NEC E88.3
- tumor necrosis factor receptor associated periodic (TRAPS) M04.1
- upward gaze H51.8
- uremia, chronic N18.9
- urethral N34.3
- urohepatic K76.7
- usher Q99.819
- vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic (VEXAS) M04.3
- vago-hypoglossal G52.7
- vanishing twin of one fetus or more O31.4
- vascular NEC in cerebrovascular disease G46.8
- vasoconstriction, reversible cerebrovascular I67.841
- vasomotor I73.9
- vasospastic (traumatic) T75.22
- vasovagal R55
- van Buchem's M85.2
- van der Hoeve's Q78.0
- VATER Q87.2
- velo-cardio-facial Q93.81
- vena cava (inferior) (superior) (obstruction) I87.1
- vertebro-basilar artery G45.0
- vertebrogenic (pain) M54.89
- VEXAS (vacuoles, E1 ubiquitin-activating enzyme, X-linked, autoinflammatory, somatic) M04.3
- Vinson-Plummer D50.1
- virus B34.9
- visceral larva migrans B83.0
- visual disorientation H53.8
- vitamin B6 deficiency E53.1
- vitreal corneal H59.01
- vitreous (touch) H59.01
- Vogt-Koyanagi H20.82
- Volkmann's T79.6
- von Hippel-Lindau Q85.83
- von Schroetter's I82.890
- Waldenström-Kjellberg D50.1
- Wallenberg's G46.3
- wasting (syndrome) due to underlying condition E88.A
- water retention E87.79
- Waterhouse (-Friderichsen) A39.1
- Weber-Gubler G46.3
- Weber-Leyden G46.3
- Weber's G46.3
- Wegener's M31.30
- Weingarten's (tropical eosinophilia) J82.89
- Weiss-Baker G90.09
- Werdnig-Hoffman G12.0
- Wermer's E31.21
- Werner's E34.8
- Wernicke-Korsakoff (nonalcoholic) F04
- Westphal-Strümpell E83.01
- whiplash S13.4
- whistling face Q87.0
- Wilkie's K55.1
- Wilkinson-Sneddon L13.1
- Williams Q93.82
- Wilson's (hepatolenticular degeneration) E83.01
- Wiskott-Aldrich D82.0
- Woakes' (ethmoiditis) J33.1
- Wright's (hyperabduction) G54.0
- X I20.9
- XXXX Q97.1
- XXXXX Q97.1
- XXXXY Q98.1
- XXY Q98.0
- Yao M04.8
- yellow nail L60.5
- Zahorsky's B08.5
- Zellweger syndrome E71.510
- Zellweger-like syndrome E71.541
Index entries, exactly as the book files them. This says they are listed together — not that any of them is documented in your chart.
How to use this page
Everything the published sources say about one code, on one page.
- Read the Excludes1 block first — it is the one that stops you coding this at all alongside another code.
- Excludes2, Code first, Use additional and Includes follow. A note inherited from a parent category is labelled with the category it came from, so you can see why it applies.
- Official Guidelines sit below. "Guidelines naming this code" cite the code or a range containing it; "Chapter guidance" is the general guidance for its chapter and is the weaker signal.
- Guideline text is quoted verbatim with its section number and page, so you can check it against the published document.
- Risk-model chips show which published CMS models map this code.
What this page does not do
- Guidance is quoted, never paraphrased — a paraphrase of a coding rule is a different rule.
- Medication candidates, where shown, are matched by condition *name* and are offered as candidates for you to judge. They are not "the drugs for this code".
Exclusions9never code together
- congenital malformation of face NOS (Q18.-)Q18.-
- congenital malformation syndromes classified to Q87.-Q87.-
- dentofacial anomalies [including malocclusion] (M26.-)M26.-
- musculoskeletal deformities of head and face (Q67.0-Q67.4)Q67.0-Q67.4
- skull defects associated with congenital anomalies of brain such as:
- anencephaly (Q00.0)Q00.0
- encephalocele (Q01.-)Q01.-
- hydrocephalus (Q03.-)Q03.-
- microcephaly (Q02)Q02
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Instructional notes2
- Franceschetti syndrome
- Treacher Collins syndrome
Official Guidelines2names this code
ICD-10-CM Official Guidelines for Coding and Reporting, quoted in full. Published by CMS and NCHS; in the public domain.
Assign an appropriate code(s) from categories Q00-QA1, Congenital malformations, deformations, and chromosomal abnormalities when a malformation/deformation or chromosomal abnormality is documented. A malformation/deformation/or chromosomal abnormality may be the principal/first-listed diagnosis on a record or a secondary diagnosis. When a malformation/deformation or chromosomal abnormality does not have a unique code assignment, assign additional code(s) for any manifestations that may be present. When the code assignment specifically identifies the malformation/deformation or chromosomal abnormality, manifestations that are an inherent component of the anomaly should not be coded separately. Additional codes should be assigned for manifestations that are not an inherent component. Codes from Chapter 17 may be used throughout the life of the patient. If a congenital malformation or deformity has been corrected, a personal history code should be used to identify the history of the malformation or deformity. Although present at birth, a malformation/deformation/or chromosomal abnormality may not be identified until later in life. Whenever the condition is diagnosed by the provider, it is appropriate to assign a code from codes Q00-QA1. For the birth admission, the appropriate code from category Z38, Liveborn infants, according to place of birth and type of delivery, should be sequenced as the principal diagnosis, followed by any congenital anomaly codes, Q00- QA1.
Index entries leading here4
Alongside this code7same parent — Q75
Additional references
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.