M04.2
Cryopyrin-associated periodic syndromes
Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 11 never code together
M00-M99chapter
Excludes2
- arthropathic psoriasis (L40.5-)L40.5-
- certain conditions originating in the perinatal period (P04-P96)P04-P96
- certain infectious and parasitic diseases (A00-B99)A00-B99
- compartment syndrome (traumatic) (T79.A-)T79.A-
- complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)Q00-Q99
- endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
- injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
- neoplasms (C00-D49)C00-D49
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 7
M04.2code
Inclusion terms
- Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
- Familial cold autoinflammatory syndrome
- Familial cold urticaria
- Muckle-Wells syndrome
- Neonatal onset multisystemic inflammatory disorder [NOMID]
M00-M25block
Includes
- Disorders affecting predominantly peripheral (limb) joints
M00-M99chapter
Notes
- Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
Index entries leading here 5
Alongside this code 3 same parent — M04
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.