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D68.2

Hereditary deficiency of other clotting factors

Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 12 never code together
D68code
Excludes1
  • abnormal coagulation profile NOS (R79.1)R79.1
Excludes2
  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)O00-O07O08.1
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)O45.0O46.0O67.0O72.3
D50-D89chapter
Excludes2
  • autoimmune disease (systemic) NOS (M35.9)M35.9
  • certain conditions originating in the perinatal period (P00-P96)P00-P96
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
  • endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
  • human immunodeficiency virus [HIV] disease (B20)B20
  • injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
  • neoplasms (C00-D49)C00-D49
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94

Excludes1 — never code together. The excluded condition and this one are mutually exclusive.

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 13
D68.2code
Inclusion terms
  • AC globulin deficiency
  • Congenital afibrinogenemia
  • Deficiency of factor I [fibrinogen]
  • Deficiency of factor II [prothrombin]
  • Deficiency of factor V [labile]
  • Deficiency of factor VII [stable]
  • Deficiency of factor X [Stuart-Prower]
  • Deficiency of factor XII [Hageman]
  • Deficiency of factor XIII [fibrin stabilizing]
  • Dysfibrinogenemia (congenital)
  • Hypoproconvertinemia
  • Owren's disease
  • Proaccelerin deficiency
Index entries leading here 17
  • Absence (of) (organ or part) (complete or partial)
    • fibrinogen (congenital) D68.2
  • Deficiency, deficient
    • accelerator globulin (Ac G) (blood) D68.2
    • AC globulin (congenital) (hereditary) D68.2
    • activating factor (blood) D68.2
    • autoprothrombin
    • coagulation NOS D68.9
      • clotting factor NEC D68.2
    • clotting factor NEC (hereditary) D68.2
    • contact factor D68.2
    • Laki-Lorand factor D68.2
    • proaccelerin (congenital) (hereditary) D68.2
    • proconvertin factor (congenital) (hereditary) D68.2
    • prothrombin (congenital) (heredItary) D68.2
    • SPCA (factor VII) D68.2
    • stable factor (congenital) (hereditary) D68.2
    • Stuart-Prower (factor X) D68.2
    • thrombokinase D68.2
    • Prower factor D68.2
    • factor — see also Deficiency, coagulation
      • Hageman D68.2
      • I (congenital) (hereditary) D68.2
      • II (congenital) (hereditary) D68.2
      • V (congenital) (hereditary) D68.2
      • VII (congenital) (hereditary) D68.2
      • X (congenital) (hereditary) D68.2
      • XII (congenital) (hereditary) D68.2
      • XIII (congenital) (hereditary) D68.2
    • fibrin-stabilizing factor (congenital) (hereditary) D68.2
    • fibrinase D68.2
    • fibrinogen (congenital) (hereditary) D68.2
    • glass factor D68.2
    • Hageman factor D68.2
    • labile factor (congenital) (hereditary) D68.2
  • Afibrinogenemia D68.8
  • Defect, defective Q89.9
    • coagulation (factor) D68.9
    • Hageman (factor) D68.2
    • fibrin polymerization D68.2
  • Fibrinogenopenia D68.8
  • Hypofibrinogenemia D68.8
    • congenital (hereditary) D68.2
  • Disease, diseased — see also Syndrome
    • Stuart's (congenital factor X deficiency) D68.2
    • Stuart-Prower (congenital factor X deficiency) D68.2
    • Hageman (congenital factor XII deficiency) D68.2
  • Dysfibrinogenemia (congenital) D68.2
  • Fibrinopenia (hereditary) D68.2
  • Hageman's factor defect, deficiency or disease D68.2
  • Hypoproconvertinemia, congenital (hereditary) D68.2
  • Hypoprothrombinemia (congenital) (hereditary) (idiopathic) D68.2
  • Syndrome — see also Disease
  • Owren's disease or syndrome (parahemophilia) D68.2
  • Parahemophilia D68.2
  • Stuart deficiency disease (factor X) D68.2
  • Stuart-Prower factor deficiency (factor X) D68.2
Alongside this code 8 same parent — D68
Medications 1

MED-RT files conditions by MeSH, which carves the world differently from ICD-10. These are name matches on this code's description, offered as candidates — not as an assertion that they are this code.

Additional references
AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

CMS22HCC48 CMS28HCC112 ESRD21HCC48 ESRD24HCC48

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This code

Billable
yes
Code set
FY2026
Parent
D68
Block
D65-D69
Siblings
8

Present FY2024–FY2027.