D76.3
Other histiocytosis syndromes
Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 24 never code together
D76code
Excludes1
- (Abt-) Letterer-Siwe disease (C96.0)C96.0
- eosinophilic granuloma (C96.6)C96.6
- Hand-Schüller-Christian disease (C96.5)C96.5
- histiocytic medullary reticulosis (C96.9)C96.9
- histiocytic sarcoma (C96.A)C96.A
- histiocytosis X, multifocal (C96.5)C96.5
- histiocytosis X, unifocal (C96.6)C96.6
- Langerhans-cell histiocytosis, multifocal (C96.5)C96.5
- Langerhans-cell histiocytosis NOS (C96.6)C96.6
- Langerhans-cell histiocytosis, unifocal (C96.6)C96.6
- leukemic reticuloendotheliosis (C91.4-)C91.4-
- lipomelanotic reticulosis (I89.8)I89.8
- malignant histiocytosis (C96.A)C96.A
- malignant reticulosis (C86.0)C86.0
- nonlipid reticuloendotheliosis (C96.0)C96.0
D50-D89chapter
Excludes2
- autoimmune disease (systemic) NOS (M35.9)M35.9
- certain conditions originating in the perinatal period (P00-P96)P00-P96
- complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
- endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
- human immunodeficiency virus [HIV] disease (B20)B20
- injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
- neoplasms (C00-D49)C00-D49
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 3
D76.3code
Inclusion terms
- Reticulohistiocytoma (giant-cell)
- Sinus histiocytosis with massive lymphadenopathy
- Xanthogranuloma
Index entries leading here 6
Alongside this code 2 same parent — D76
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.