The classification presumes a causal relationship between hypertension and heart involvement and between hypertension and kidney involvement, as the two conditions are linked by the term “with” in the Alphabetic Index. These conditions should be coded as related even in the absence of provider documentation explicitly linking them, unless the documentation clearly states the conditions are unrelated. For hypertension and conditions not specifically linked by relational terms such as “with,” “associated with” or “due to” in the classification, provider documentation must link the conditions in order to code them as related.
I08.9
BookmarkRheumatic multiple valve disease, unspecified
Filed alongside this entry 585
under Disease, diseased
- absorbent system I87.8
- acid-peptic K30
- Acosta's T70.29
- Adams-Stokes (-Morgagni) (syncope with heart block) I45.9
- Addison's anemia (pernicious) D51.0
- adenoids (and tonsils) J35.9
- adrenal (capsule) (cortex) (gland) (medullary) E27.9
- ainhum L94.6
- akamushi (scrub typhus) A75.3
- Albers-Schönberg (marble bones) Q78.2
- Alexander G31.86
- alimentary canal K63.9
- alligator-skin Q80.9
- alpha heavy chain C88.3
- alpine T70.29
- altitude T70.20
- alveoli, teeth K08.9
- Alzheimer's G30.9
- Andersen's (glycogenosis IV) E74.09
- Andes T70.29
- Andrews' (bacterid) L08.89
- angiospastic I73.9
- antiglomerular basement membrane (anti- GBM) antibody M31.0
- Antopol E74.05
- anus K62.9
- aorta (nonsyphilitic) I77.9
- aortic (heart) (valve) I35.9
- Apollo B30.3
- appendix K38.9
- aqueous (chamber) H21.9
- arterial I77.9
- arteriolar (generalized) (obliterative) I77.9
- artery I77.9
- arthropod-borne NOS (viral) A94
- atticoantral, chronic H66.20
- Australian X A83.4
- autoimmune (systemic) NOS M35.9
- autoinflammatory M04.9
- Ayerza's (pulmonary artery sclerosis with pulmonary hypertension) I27.0
- Babington's (familial hemorrhagic telangiectasia) I78.0
- bacterial A49.9
- Baelz's (cheilitis glandularis apostematosa) K13.0
- bagasse J67.1
- Bang's (brucella abortus) A23.1
- Bannister's T78.3
- Barraquer (-Simons') (progressive lipodystrophy) E88.11
- Bartholin's gland N75.9
- basal ganglia G25.9
- Bateman's B08.1
- Batten-Steinert G71.11
- Battey A31.0
- Beard's (neurasthenia) F48.8
- behavioral, organic F07.9
- Beigel's (white piedra) B36.2
- Bernard-Soulier (thrombopathy) D69.19
- Biermer's (pernicious anemia) D51.0
- bile duct (common) (hepatic) K83.9
- biliary (tract) K83.9
- bird fancier's J67.2
- black lung J60
- bladder N32.9
- bleeder's D66
- blood D75.9
- Blount M92.51
- Bodechtel-Guttmann (subacute sclerosing panencephalitis) A81.1
- bone-marrow D75.9
- Borna A83.9
- Bornholm (epidemic pleurodynia) B33.0
- Bouchard's (myopathic dilatation of the stomach) K31.0
- Bouillaud's (rheumatic heart disease) I01.9
- Bourneville (-Brissaud) (tuberous sclerosis) Q85.1
- Bouveret (-Hoffmann) (paroxysmal tachycardia) I47.9
- bowel K63.9
- brain G93.9
- breast N64.9
- Bretonneau's (diphtheritic malignant angina) A36.0
- Brill's (recrudescent typhus) A75.1
- Brill-Zinsser (recrudescent typhus) A75.1
- Brocq-Duhring (dermatitis herpetiformis) L13.0
- bronchopulmonary J98.4
- bronchus NEC J98.09
- bronze Addison's E27.1
- budgerigar fancier's J67.2
- bullous L13.9
- Buerger's (thromboangiitis obliterans) I73.1
- Bürger-Grütz (essential familial hyperlipemia) E78.3
- caisson T70.3
- Canavan E75.28
- capillaries I78.9
- Carapata A68.0
- carcinoid E34.00
- cardiopulmonary, chronic I27.9
- cardiovascular (atherosclerotic) I25.10
- Castellani's A69.8
- Castleman (unicentric) (multicentric) D47.Z2
- cat-scratch A28.1
- Cavare's (familial periodic paralysis) G72.3
- cecum K63.9
- celiac (adult) (infantile) (with steatorrhea) K90.0
- cellular tissue L98.9
- central core G71.29
- cerebrospinal G96.9
- cerebrovascular I67.9
- cervix (uteri) (noninflammatory) N88.9
- Chabert's A22.9
- Chédiak-Steinbrinck (-Higashi) (congenital gigantism of peroxidase granules) E70.330
- chest J98.9
- Chiari's (hepatic vein thrombosis) I82.0
- Chicago B40.9
- Chignon B36.8
- chigo, chigoe B88.1
- childhood granulomatous D71.8
- Chinese liver fluke B66.1
- chlamydial A74.9
- cholecystic K82.9
- choroid H31.9
- Christmas D67
- chronic bullous of childhood L12.2
- chylomicron retention E78.3
- ciliary body H21.9
- circulatory (system) NEC I99.8
- collagen NOS (nonvascular) (vascular) M35.9
- colon K63.9
- colonic inflammatory bowel, unclassified (IBDU) K52.3
- compressed air T70.3
- Concato's (pericardial polyserositis) A19.9
- conjunctiva H11.9
- connective tissue, systemic (diffuse) M35.9
- Conor and Bruch's (boutonneuse fever) A77.1
- Cori's (glycogenosis III) E74.03
- corkhandler's or corkworker's J67.3
- cornea H18.9
- corpus cavernosum N48.9
- COVID-19 U07.1
- coxsackie (virus) NEC B34.1
- cranial nerve NOS G52.9
- Crocq's (acrocyanosis) I73.89
- Curschmann G71.11
- cytomegalic inclusion (generalized) B25.9
- cytomegaloviral B25.9
- Daae (-Finsen) (epidemic pleurodynia) B33.0
- Danon E74.05
- Débove's (splenomegaly) R16.1
- Degos' I77.89
- demyelinating, demyelinizating (nervous system) G37.9
- dense deposit N05.6
- de Quervain's (tendon sheath) M65.4
- Devergie's (pityriasis rubra pilaris) L44.0
- Devic's G36.0
- diaphorase deficiency D74.0
- diaphragm J98.6
- diarrheal, infectious NEC A09
- digestive system K92.9
- Dubois (thymus) A50.59
- Duchenne-Griesinger G71.01
- ductless glands E34.9
- Duhring's (dermatitis herpetiformis) L13.0
- duodenum K31.9
- Dupré's (meningism) R29.1
- Dupuytren's (muscle contracture) M72.0
- Durand-Nicholas-Favre (climatic bubo) A55
- Duroziez's (congenital mitral stenosis) Q23.2
- Ebola (virus) A98.4
- Ebstein's heart Q22.5
- echovirus NEC B34.1
- Eddowes' (brittle bones and blue sclera) Q78.0
- edentulous (alveolar) ridge K06.9
- Edsall's T67.2
- Eichstedt's (pityriasis versicolor) B36.0
- Eisenmenger's (irreversible) I27.83
- Ellis-van Creveld (chondroectodermal dysplasia) Q77.6
- end stage renal (ESRD) N18.6
- endocrine glands or system NEC E34.9
- endomyocardial (eosinophilic) I42.3
- English (rickets) E55.0
- enteroviral, enterovirus NEC B34.1
- epidemic B99.9
- epididymis N50.9
- Erb (-Landouzy) G71.02
- Erdheim-Chester (ECD) E88.89
- esophagus K22.9
- Eulenburg's (congenital paramyotonia) G71.19
- extrapyramidal G25.9
- eye H57.9
- eyeball H44.9
- eyeworm of Africa B74.3
- facial nerve (seventh) G51.9
- Fahr (of brain) G23.8
- fallopian tube (noninflammatory) N83.9
- familial periodic paralysis G72.3
- Fanconi ('s) D61.03
- Favre-Durand-Nicolas (climatic bubo) A55
- Fede's K14.0
- female pelvic inflammatory N73.9
- Fernels' (aortic aneurysm) I71.9
- Fiedler's (leptospiral jaundice) A27.0
- fifth B08.3
- fish-skin Q80.9
- flax-dresser's J66.1
- foot and mouth B08.8
- foot process N04.9
- Forbes' (glycogenosis III) E74.03
- Fordyce-Fox (apocrine miliaria) L75.2
- Fordyce's (ectopic sebaceous glands) (mouth) Q38.6
- Forestier's (rhizomelic pseudopolyarthritis) M35.3
- Fournier (gangrene) N49.3
- fourth B08.8
- Fox (-Fordyce) (apocrine miliaria) L75.2
- Franklin C88.2
- Frei's (climatic bubo) A55
- fungus NEC B49
- Gaisböck's (polycythemia hypertonica) D75.1
- gallbladder K82.9
- gamma heavy chain C88.2
- Gamna's (siderotic splenomegaly) D73.2
- Gamstorp's (adynamia episodica hereditaria) G72.3
- Gandy-Nanta (siderotic splenomegaly) D73.2
- ganister J62.8
- gastroesophageal reflux (GERD) K21.9
- gastrointestinal (tract) K92.9
- Gee (-Herter) (-Heubner) (-Thaysen) (nontropical sprue) K90.0
- Gerhardt's (erythromelalgia) I73.81
- Gibert's (pityriasis rosea) L42
- Gierke's (glycogenosis I) E74.01
- Gilles de la Tourette's (motor-verbal tic) F95.2
- gingiva K06.9
- gland (lymph) I89.9
- Glanzmann's (hereditary hemorrhagic thrombasthenia) D69.11
- globe H44.9
- glycogen storage E74.00
- Goldstein's (familial hemorrhagic telangiectasia) I78.0
- gonococcal NOS A54.9
- graft-versus-host (GVH) D89.813
- grainhandler's J67.8
- granulomatous (childhood) (chronic) D71.8
- Grisel's M43.6
- Gruby's (tinea tonsurans) B35.0
- Guillain-Barré G61.0
- Guinon's (motor-verbal tic) F95.2
- gum K06.9
- gynecological N94.9
- H (Hartnup's) E72.02
- Hageman (congenital factor XII deficiency) D68.2
- hair (color) (shaft) L67.9
- Hamman's (spontaneous mediastinal emphysema) J98.2
- hand, foot and mouth B08.4
- Hantavirus, with pulmonary manifestations B33.4
- Harada's H30.81
- Hartnup (pellagra-cerebellar ataxia-renal aminoaciduria) E72.02
- Hart's (pellagra-cerebellar ataxia-renal aminoaciduria) E72.02
- Hashimoto's (struma lymphomatosa) E06.3
- heart (organic) I51.9
- Heartland A93.8
- heavy chain NEC C88.2
- hematopoietic organs D75.9
- hemolytic (newborn) P55.9
- hemorrhagic D69.9
- Henoch (-Schönlein) (purpura nervosa) D69.0
- hepatobiliary K83.9
- hepatolenticular E83.01
- herpesviral, disseminated B00.7
- Hers' (glycogenosis VI) E74.09
- Herter (-Gee) (-Heubner) (nontropical sprue) K90.0
- Heubner-Herter (nontropical sprue) K90.0
- high fetal gene or hemoglobin thalassemia D56.9
- hip (joint) M25.9
- His (-Werner) (trench fever) A79.0
- Hodgson's I71.20
- hookworm B76.9
- host-versus-graft D89.813
- human immunodeficiency virus (HIV) B20
- Huntington's G10
- Hunt's (herpetic geniculate ganglionitis) (neuralgia) B02.21
- hydroxyapatite deposition M11.00
- hypophysis E23.7
- Iceland G93.39
- I-cell E77.0
- IgG4-related D89.84
- immune D89.9
- immunoproliferative (malignant) C88.9
- inclusion B25.9
- infectious, infective B99.9
- intestine K63.9
- iris H21.9
- iron metabolism or storage E83.10
- island (scrub typhus) A75.3
- jaw M27.9
- jigger B88.1
- Jourdain's (acute gingivitis) K05.00
- Kaschin-Beck (endemic polyarthritis) M12.10
- Katayama B65.2
- Kedani (scrub typhus) A75.3
- Keshan E59
- kidney (functional) (pelvis) N28.9
- Kimura D21.9
- Kinnier Wilson's (hepatolenticular degeneration) E83.01
- Klippel-Feil (brevicollis) Q76.1
- Kok Q89.89
- Korsakoff's (nonalcoholic) F04
- Kostmann's (infantile genetic agranulocytosis) D70.0
- kuru A81.81
- Kyasanur Forest A98.2
- Lafora body G40.C09
- Lancereaux-Mathieu (leptospiral jaundice) A27.0
- Landry's G61.0
- Larrey-Weil (leptospiral jaundice) A27.0
- larynx J38.7
- Ledderhose M72.2
- legionnaires' A48.1
- Lenegre's I44.2
- lens H27.9
- Lev's (acquired complete heart block) I44.2
- Lewy body (dementia) G31.83
- Lichtheim's (subacute combined sclerosis with pernicious anemia) D51.0
- Lightwood's (renal tubular acidosis) N25.89
- Lignac's (cystinosis) E72.04
- lip K13.0
- lipid-storage E75.6
- Lipschütz's N76.6
- liver (chronic) (organic) K76.9
- Lobo's (keloid blastomycosis) B48.0
- Lobstein's (brittle bones and blue sclera) Q78.0
- Ludwig's (submaxillary cellulitis) K12.2
- lumbosacral region M53.87
- lung J98.4
- Lutembacher's (atrial septal defect with mitral stenosis) Q21.19
- Lyme A69.20
- lymphatic (gland) (system) (channel) (vessel) I89.9
- lymphoproliferative D47.9
- Magitot's M27.2
- Manson's B65.1
- maple bark J67.6
- maple-syrup-urine E71.0
- Marburg (virus) A98.3
- Marion's (bladder neck obstruction) N32.0
- Mathieu's (leptospiral jaundice) A27.0
- Maxcy's A75.2
- McArdle (-Schmid-Pearson) (glycogenosis V) E74.04
- mediastinum J98.59
- medullary center (idiopathic) (respiratory) G93.89
- Meige's (chronic hereditary edema) Q82.0
- mental F99
- mesenchymal M35.9
- mesenteric embolic K55.039
- metabolic, metabolism E88.9
- metal-polisher's J62.8
- metastatic C79.9
- Mikulicz' (dryness of mouth, absent or decreased lacrimation) K11.8
- Milroy's (chronic hereditary edema) Q82.0
- minicore G71.29
- Minor's G95.19
- Minot's (hemorrhagic disease, newborn) P53
- Mitchell's (erythromelalgia) I73.81
- mitral (valve) I05.9
- mixed connective tissue M35.1
- MOG antibody G37.81
- moldy hay J67.0
- Monge's T70.29
- Morgagni-Adams-Stokes (syncope with heart block) I45.9
- Morgagni's (syndrome) (hyperostosis frontalis interna) M85.2
- Morvan's G60.8
- motor neuron (bulbar) (mixed type) (spinal) G12.20
- moyamoya I67.5
- mu heavy chain disease C88.2
- multicore G71.29
- multiminicore G71.29
- mushroom workers' J67.5
- mycotic B49
- myelin oligodendrocyte glycoprotein antibody G37.81
- myelodysplastic C94.6
- myelodysplastic/myeloproliferative neoplasm, unclassifiable C94.6
- myeloproliferative D47.1
- myocardium, myocardial I51.5
- myoneural G70.9
- Naegeli's Q82.8
- nails L60.9
- Nairobi (sheep virus) A93.8
- nasal J34.9
- nemaline body G71.21
- nervous system G98.8
- neuromuscular system G70.9
- Newcastle B30.8
- Nicolas (-Durand)-Favre (climatic bubo) A55
- nipple N64.9
- Nishimoto (-Takeuchi) I67.5
- nonarthropod-borne NOS (viral) B34.9
- nonautoimmune hemolytic D59.4
- Nonne-Milroy-Meige (chronic hereditary edema) Q82.0
- nose J34.9
- nutritional E63.9
- oast-house-urine E72.19
- obliterative vascular I77.1
- Opitz's (congestive splenomegaly) D73.2
- Oriental liver fluke B66.1
- Oriental lung fluke B66.4
- Ormond's N13.5
- Oropouche virus A93.0
- Osler-Rendu (familial hemorrhagic telangiectasia) I78.0
- osteofibrocystic E21.0
- Otto's M24.7
- ovary (noninflammatory) N83.9
- p110d-activating mutation causing senescent T cells, lymphadenopathy, and immunodeficiency [PASLI] D81.82
- pancreas K86.9
- panvalvular I08.9
- parametrium (noninflammatory) N83.9
- parasitic B89
- parathyroid (gland) E21.5
- Parkinson's G20.A1
- parodontal K05.6
- Parrot's (syphilitic osteochondritis) A50.02
- Paxton's (white piedra) B36.2
- pelvis, pelvic K6A.8
- penis N48.9
- periapical tissues NOS K04.90
- periodontal K05.6
- peritoneum K66.9
- persistent mucosal (middle ear) H66.20
- pharynx J39.2
- photochromogenic (acid-fast bacilli) (pulmonary) A31.0
- Pick's G31.01
- pigeon fancier's J67.2
- pineal gland E34.8
- Pinkus' (lichen nitidus) L44.1
- pinworm B80
- Piry virus A93.8
- pituitary (gland) E23.7
- pituitary-snuff-taker's J67.8
- pleura (cavity) J94.9
- pneumatic drill (hammer) T75.21
- Pollitzer's (hidradenitis suppurativa) L73.2
- polyethylene T84.05
- Pompe's (glycogenosis II) E74.02
- Posadas-Wernicke B38.9
- prepuce N47.8
- Pringle's (tuberous sclerosis) Q85.1
- prion, central nervous system A81.9
- prostate N42.9
- protozoal B64
- pseudo-Hurler's E77.0
- psychiatric F99
- Puente's (simple glandular cheilitis) K13.0
- puerperal O90.89
- pulp (dental) NOS K04.90
- pulseless M31.4
- Putnam's (subacute combined sclerosis with pernicious anemia) D51.0
- Pyle (-Cohn) (metaphyseal dysplasia) Q78.5
- ragpicker's or ragsorter's A22.1
- rectum K62.9
- Refsum's (heredopathia atactica polyneuritiformis) G60.1
- renal (functional) (pelvis) N28.9
- Rendu-Osler-Weber (familial hemorrhagic telangiectasia) I78.0
- respiratory (tract) J98.9
- retina, retinal H35.9
- rickettsial NOS A79.9
- Riga (-Fede) (cachectic aphthae) K14.0
- Ritter's L00
- Rivalta's (cervicofacial actinomycosis) A42.2
- Robles' (onchocerciasis) B73.01
- rod body G71.21
- Roger's (congenital interventricular septal defect) Q21.0
- Rosenthal's (factor XI deficiency) D68.1
- Rossbach's (hyperchlorhydria) K31.89
- Ross River B33.1
- Runeberg's (progressive pernicious anemia) D51.0
- sacroiliac NEC M53.3
- salivary gland or duct K11.9
- sandworm B76.9
- Schönlein (-Henoch) (purpura rheumatica) D69.0
- Schwalbe-Ziehen-Oppenheim G24.1
- Schwartz-Jampel G71.13
- sclera H15.9
- scrofulous (tuberculous) A18.2
- scrotum N50.9
- sebaceous glands L73.9
- seminal vesicle N50.9
- serum NEC T80.69
- sexually transmitted A64
- Sézary C84.1
- shimamushi (scrub typhus) A75.3
- shipyard B30.0
- sickle-cell D57.1
- silo-filler's J68.8
- simian B B00.4
- Simons' (progressive lipodystrophy) E88.11
- sin nombre virus B33.4
- Sirkari's B55.0
- sixth B08.20
- skin L98.9
- slim (HIV) B20
- small vessel I73.9
- Sneddon-Wilkinson (subcorneal pustular dermatosis) L13.1
- South African creeping B88.09
- spinal (cord) G95.9
- spinocerebellar (hereditary) G11.9
- spleen D73.9
- Startle Q89.89
- Steinert's G71.11
- Sticker's (erythema infectiosum) B08.3
- Stokes-Adams (syncope with heart block) I45.9
- stomach K31.9
- stonemason's J62.8
- striatopallidal system NEC G25.89
- Stuart-Prower (congenital factor X deficiency) D68.2
- Stuart's (congenital factor X deficiency) D68.2
- supporting structures of teeth K08.9
- suprarenal (capsule) (gland) E27.9
- sweat glands L74.9
- Sweeley-Klionsky E75.21
- swimming-pool granuloma A31.1
- Sylvest's (epidemic pleurodynia) B33.0
- sympathetic nervous system G90.9
- systemic tissue mast cell D47.02
- tanapox (virus) B08.71
- Tangier E78.6
- Tarral-Besnier (pityriasis rubra pilaris) L44.0
- Tauri's E74.09
- terminal vessel I73.9
- testis N50.9
- Thaysen-Gee (nontropical sprue) K90.0
- Thomsen G71.12
- throat J39.2
- thymus (gland) E32.9
- thyroid (gland) E07.9
- Tietze's M94.0
- tongue K14.9
- tonsils, tonsillar (and adenoids) J35.9
- tooth, teeth K08.9
- Tourette's F95.2
- trachea NEC J39.8
- tricuspid I07.9
- triglyceride-storage E75.5
- tsutsugamushi A75.3
- tube (fallopian) (noninflammatory) N83.9
- tubo-ovarian (noninflammatory) N83.9
- tubulo-interstitial N15.9
- Uhl's Q24.8
- Underwood's (sclerema neonatorum) P83.0
- ureter N28.9
- urethra N36.9
- urinary (tract) N39.9
- uterus (noninflammatory) N85.9
- uveal tract (anterior) H21.9
- vagabond's B85.1
- vagina, vaginal (noninflammatory) N89.9
- valve, valvular I38
- van Creveld-von Gierke (glycogenosis I) E74.01
- vas deferens N50.9
- vascular I99.9
- vasomotor I73.9
- vasospastic I73.9
- vein I87.9
- venereal A64
- viral, virus B34.9
- vitreous H43.9
- vocal cord J38.3
- Volkmann's, acquired T79.6
- von Eulenburg's (congenital paramyotonia) G71.19
- von Gierke's (glycogenosis I) E74.01
- von Willebrand (-Jürgens) (angiohemophilia) D68.00
- Vrolik's (osteogenesis imperfecta) Q78.0
- vulva (noninflammatory) N90.9
- Wallgren's (obstruction of splenic vein with collateral circulation) I87.8
- Wassilieff's (leptospiral jaundice) A27.0
- wasting NEC E88.A
- Waterhouse-Friderichsen A39.1
- Wegner's (syphilitic osteochondritis) A50.02
- Weil's (leptospiral jaundice of lung) A27.0
- Weir Mitchell's (erythromelalgia) I73.81
- Werdnig-Hoffmann G12.0
- Wermer's E31.21
- Werner-His (trench fever) A79.0
- Werner-Schultz (neutropenic splenomegaly) D73.81
- Wernicke-Posadas B38.9
- whipworm B79
- white blood cells D72.9
- white matter R90.82
- white-spot, meaning lichen sclerosus et atrophicus L90.0
- Wilkie's K55.1
- Wilkinson-Sneddon (subcorneal pustular dermatosis) L13.1
- Wilson's (hepatolenticular degeneration) E83.01
- woolsorter's A22.1
- yaba monkey tumor B08.72
- yaba pox (virus) B08.72
- Zika virus A92.5
- zoonotic, bacterial A28.9
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What this page does not do
- Guidance is quoted, never paraphrased — a paraphrase of a coding rule is a different rule.
- Medication candidates, where shown, are matched by condition *name* and are offered as candidates for you to judge. They are not "the drugs for this code".
Exclusions13never code together
- certain conditions originating in the perinatal period (P04-P96)P04-P96
- certain infectious and parasitic diseases (A00-B99)A00-B99
- complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)Q00-Q99
- endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
- injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
- neoplasms (C00-D49)C00-D49
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94
- systemic connective tissue disorders (M30-M36)M30-M36
- transient cerebral ischemic attacks and related syndromes (G45.-)G45.-
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes1
- multiple valve diseases specified as rheumatic or unspecified
Official Guidelines24
ICD-10-CM Official Guidelines for Coding and Reporting, quoted in full. Published by CMS and NCHS; in the public domain.
Hypertension with heart conditions classified to I50.-, Heart failure, I51.4, Myocarditis, unspecified, I51.89, Other ill-defined heart diseases, and I51.9, Heart disease, unspecified, is assigned to a code from category I11, Hypertensive heart disease. Use additional code(s) from category I50, Heart failure, or I51, Complications and ill-defined descriptions of heart disease, to identify the heart condition. Hypertension with heart conditions classified to I51.5, Myocardial degeneration, or I51.7, Cardiomegaly, is assigned to a code from category I11, Hypertensive heart disease. No additional code is assigned to identify the specific heart condition. The same heart conditions (I50.-, I51.4-I51.7, I51.89, I51.9) with hypertension are coded separately if the provider has documented they are unrelated to the hypertension. The applicable hypertension code I10, Essential (primary) hypertension, or a code from category I15, Secondary hypertension, should be assigned. Sequence according to the circumstances of the admission/encounter.
Assign codes from category I12, Hypertensive chronic kidney disease, when both hypertension and a condition classifiable to category N18, Chronic kidney disease (CKD), are present. CKD should not be coded as hypertensive if the provider indicates the CKD is not related to the hypertension. The appropriate code from category N18 should be used as a secondary code with a code from category I12 to identify the stage of chronic kidney disease. See Section I.C.14. Chronic kidney disease. If a patient has hypertensive chronic kidney disease and acute renal failure, the acute renal failure should also be coded. Sequence according to the circumstances of the admission/encounter.
The codes in category I13, Hypertensive heart and chronic kidney disease, are combination codes that include hypertension, heart disease and chronic kidney disease. Assign codes from combination category I13, Hypertensive heart and chronic kidney disease, when there is hypertension with both heart and chronic kidney disease. If heart failure is present, assign an additional code from category I50 to identify the type of heart failure. The appropriate code from category N18, Chronic kidney disease, should be used as a secondary code with a code from category I13 to identify the stage of chronic kidney disease. See Section I.C.14. Chronic kidney disease. The Includes note at I13 specifies that the conditions included at I11 and I12 are included together in I13. If a patient has hypertension, heart disease and chronic kidney disease, then a code from I13 should be used, not codes from I11 or I12, For patients with both acute renal failure and chronic kidney disease, the acute renal failure should also be coded. Sequence according to the circumstances of the admission/encounter.
For hypertensive cerebrovascular disease, first assign the appropriate code from categories I60-I69, followed by the appropriate hypertension code.
Subcategory H35.0, Background retinopathy and retinal vascular changes, should be used along with a code from categories I10 – I15, in the Hypertensive diseases section, to include the systemic hypertension. The sequencing is based on the reason for the encounter.
Secondary hypertension is due to an underlying condition. Two codes are required: one to identify the underlying etiology and one from category I15 to identify the hypertension. Sequencing of codes is determined by the reason for admission/encounter.
Assign a code from category I16, Hypertensive crisis, for documented hypertensive urgency, hypertensive emergency or unspecified hypertensive crisis. Code also any identified hypertensive disease (I10- I15). The sequencing is based on the reason for the encounter.
Pulmonary hypertension is classified to category I27, Other pulmonary heart diseases. For secondary pulmonary hypertension (I27.1, I27.2-), code also any associated conditions or adverse effects of drugs or toxins. The sequencing is based on the reason for the encounter, except for adverse effects of drugs (See Section I.C.19.e.).
Resistant hypertension refers to blood pressure of a patient with hypertension that remains above goal in spite of the use of antihypertensive medications. Assign code I1A.0, Resistant hypertension, as an additional code when apparent treatment resistant hypertension, treatment resistant hypertension, or true resistant hypertension is documented by the provider. A code for the specific type of existing hypertension is sequenced first, if known.
Assign code R03.0, Elevated blood pressure reading without diagnosis of hypertension, unless patient has an established diagnosis of hypertension. Assign code O13.-, Gestational [pregnancy-induced] hypertension without significant proteinuria, or O14.-, Pre-eclampsia, for transient hypertension of pregnancy.
This diagnostic statement usually refers to an existing state of hypertension under control by therapy. Assign the appropriate code from categories I10-I15, Hypertensive diseases.
Uncontrolled hypertension may refer to untreated hypertension or hypertension not responding to current therapeutic regimen. In either case, assign the appropriate code from categories I10-I15, Hypertensive diseases.
ICD-10-CM has combination codes for atherosclerotic heart disease with angina pectoris. The subcategories for these codes are I25.11, Atherosclerotic heart disease of native coronary artery with angina pectoris and I25.7, Atherosclerosis of coronary artery bypass graft(s) and coronary artery of transplanted heart with angina pectoris. When using one of these combination codes it is not necessary to use an additional code for angina pectoris. A causal relationship can be assumed in a patient with both atherosclerosis and angina pectoris, unless the documentation indicates the angina is due to something other than the atherosclerosis. If a patient with coronary artery disease is admitted due to an acute myocardial infarction (AMI), the AMI should be sequenced before the coronary artery disease. See Section I.C.9. Acute myocardial infarction (AMI)
Medical record documentation should clearly specify the cause- and-effect relationship between the medical intervention and the cerebrovascular accident in order to assign a code for intraoperative or postprocedural cerebrovascular accident. Proper code assignment depends on whether it was an infarction or hemorrhage and whether it occurred intraoperatively or postoperatively. If it was a cerebral hemorrhage, code assignment depends on the type of procedure performed.
Category I69 is used to indicate conditions classifiable to categories I60- I67 as the causes of sequela (neurologic deficits), themselves classified elsewhere. These “late effects” include neurologic deficits that persist after initial onset of conditions classifiable to categories I60-I67. The neurologic deficits caused by cerebrovascular disease may be present from the onset or may arise at any time after the onset of the condition classifiable to categories I60-I67. Codes from category I69, Sequelae of cerebrovascular disease, that specify hemiplegia, hemiparesis and monoplegia identify whether the dominant or nondominant side is affected. Should the affected side be documented, but not specified as dominant or nondominant, and the classification system does not indicate a default, code selection is as follows: • For ambidextrous patients, the default should be dominant. • If the left side is affected, the default is non-dominant. • If the right side is affected, the default is dominant.
Codes from category I69 may be assigned on a health care record with codes from I60-I67, if the patient has a current cerebrovascular disease and deficits from an old cerebrovascular disease.
ischemic attack (TIA) and cerebral infarction (Z86.73) Codes from category I69 should not be assigned if the patient does not have neurologic deficits. See Section I.C.21.4. History (of) for use of personal history codes
ST elevation myocardial infarction (NSTEMI) The ICD-10-CM codes for type 1 acute myocardial infarction (AMI) identify the site, such as anterolateral wall or true posterior wall. Subcategories I21.0-I21.2 and code I21.3 are used for type 1 ST elevation myocardial infarction (STEMI). Code I21.4, Non-ST elevation (NSTEMI) myocardial infarction, is used for type 1 non-ST elevation myocardial infarction (NSTEMI) and nontransmural MIs. If a type 1 NSTEMI evolves to STEMI, assign the STEMI code. If a type 1 STEMI converts to NSTEMI due to thrombolytic therapy, it is still coded as STEMI. For encounters occurring while the myocardial infarction is equal to, or less than, four weeks old, including transfers to another acute setting or a postacute setting, and the myocardial infarction meets the definition for “other diagnoses” (see Section III, Reporting Additional Diagnoses), codes from category I21 may continue to be reported. For encounters after the 4-week time frame and the patient is still receiving care related to the myocardial infarction, the appropriate aftercare code should be assigned, rather than a code from category I21. For old or healed myocardial infarctions not requiring further care, code I25.2, Old myocardial infarction, may be assigned.
Code I21.9, Acute myocardial infarction, unspecified, is the default for unspecified acute myocardial infarction or unspecified type. If only type 1 STEMI or transmural MI without the site is documented, assign code I21.3, ST elevation (STEMI) myocardial infarction of unspecified site.
provided If an AMI is documented as nontransmural or subendocardial, but the site is provided, it is still coded as a subendocardial AMI. See Section I.C.21.3. for information on coding status post administration of tPA in a different facility within the last 24 hours.
A code from category I22, Subsequent ST elevation (STEMI) and non- ST elevation (NSTEMI) myocardial infarction, is to be used when a patient who has suffered a type 1 or unspecified AMI has a new AMI within the 4 week time frame of the initial AMI. A code from category I22 must be used in conjunction with a code from category I21. The sequencing of the I22 and I21 codes depends on the circumstances of the encounter. Do not assign code I22 for subsequent myocardial infarctions other than type 1 or unspecified. For subsequent type 2 AMI assign only code I21.A1. For subsequent type 4 or type 5 AMI, assign only code I21.A9. If a subsequent myocardial infarction of one type occurs within 4 weeks of a myocardial infarction of a different type, assign the appropriate codes from category I21 to identify each type. Do not assign a code from I22. Codes from category I22 should only be assigned if both the initial and subsequent myocardial infarctions are type 1 or unspecified.
The ICD-10-CM provides codes for different types of myocardial infarction. Type 1 myocardial infarctions are assigned to codes I21.0- I21.4. Type 2 myocardial infarction (myocardial infarction due to demand ischemia or secondary to ischemic imbalance) is assigned to code I21.A1, Myocardial infarction type 2 with the underlying cause coded first, if applicable. Do not assign code I24.89, Other forms of acute ischemic heart disease, for the demand ischemia. If a type 2 AMI is described as NSTEMI or STEMI, only assign code I21.A1. Codes I21.01-I21.4 should only be assigned for type 1 AMIs. Acute myocardial infarctions type 3, 4a, 4b, 4c and 5 are assigned to code I21.A9, Other myocardial infarction type. The "Code also" and "Code first" notes should be followed related to complications, and for coding of postprocedural myocardial infarctions during or following cardiac surgery.
Dysfunction Coronary microvascular dysfunction (CMD) is a condition that impacts the microvasculature by restricting microvascular flow and increasing microvascular resistance. Code I21.B, Myocardial infarction with coronary microvascular dysfunction, is assigned for myocardial infarction with coronary microvascular disease, myocardial infarction with coronary microvascular dysfunction, and myocardial infarction with non-obstructive coronary arteries (MINOCA) with microvascular disease.
Index entries leading here3
Alongside this code5same parent — I08
Additional references
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.