Q99.81

Usher syndrome

Not billable — category only FY2026 2025-10-01 → 2026-09-30 FY2026–2027 only

Exclusions 1 never code together

Q90-Q99block

Excludes2

mitochondrial metabolic disorders (E88.4-)E88.4-

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 1

Q99.81code

Use additional code

code to identify any auditory and visual manifestations

Index entries leading here 5 filed at Q99.8

The index files this at Q99.8. The tabular extends it — laterality, staging, or the 7th character — so these entries lead to the family rather than to Q99.81 exactly.

Abnormal, abnormality, abnormalities — see also Anomaly
- chromosome, chromosomal Q99.9
  - sex Q99.8
  - specified NEC Q99.8
Additional — see also Accessory
- chromosome (s) Q99.8
Anomaly, anomalous (congenital) (unspecified type) Q89.9
- chromosomes, chromosomal Q99.9
  - specified NEC Q99.8
Syndrome — see also Disease
- due to abnormality
  - chromosomal Q99.9
    - specified NEC Q99.8
Translocation
- chromosomes NEC Q99.8

Alongside this code 1 same parent — Q99.8

Q99.89 Other specified chromosome abnormalities

Subordinate codes 5

Q99.811 Usher syndrome, type 1 Q99.812 Usher syndrome, type 2 Q99.813 Usher syndrome, type 3 Q99.818 Other Usher syndrome Q99.819 Usher syndrome, unspecified

Additional references

AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

Maps to no condition category in any loaded model.

Presence is a property of the code. Untick a model to hide it everywhere.

This code

Billable: no
Code set: FY2026
Parent: Q99.8
Block: Q90-Q99
Siblings: 1
Subordinate: 5

Present FY2026–FY2027.