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Q99.1

46, XX true hermaphrodite

Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 1 never code together
Q90-Q99block
Excludes2
  • mitochondrial metabolic disorders (E88.4-)E88.4-

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 3
Q99.1code
Inclusion terms
  • 46, XX with streak gonads
  • 46, XY with streak gonads
  • Pure gonadal dysgenesis
Index entries leading here 6
  • Karyotype
  • Hermaphrodite, hermaphroditism (true) Q56.0
    • 46,XX with streak gonads Q99.1
    • 46,XY with streak gonads Q99.1
  • Anomaly, anomalous (congenital) (unspecified type) Q89.9
    • chromosomes, chromosomal Q99.9
      • sex
        • gonadal dysgenesis (pure) Q99.1
  • Dysgenesis
    • gonadal (due to chromosomal anomaly) Q96.9
  • Syndrome — see also Disease
  • Swyer syndrome Q99.1
Alongside this code 4 same parent — Q99
Q99.0 Chimera 46, XX/46, XY Q99.2 Fragile X chromosome Q99.8 Other specified chromosome abnormalities category Q99.9 Chromosomal abnormality, unspecified
Additional references
AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

Maps to no condition category in any loaded model.

Presence is a property of the code. Untick a model to hide it everywhere.

This code

Billable
yes
Code set
FY2026
Parent
Q99
Block
Q90-Q99
Siblings
4

Present FY2024–FY2027.