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Q98.1

Klinefelter syndrome, male with more than two X chromosomes

Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 1 never code together
Q90-Q99block
Excludes2
  • mitochondrial metabolic disorders (E88.4-)E88.4-

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes

No further instructional notes apply.

Index entries leading here 3
  • Klinefelter's syndrome Q98.4
    • male with more than two X chromosomes Q98.1
  • Syndrome — see also Disease
  • XXXXY syndrome Q98.1
Alongside this code 8 same parent — Q98
Q98.0 Klinefelter syndrome karyotype 47, XXY Q98.3 Other male with 46, XX karyotype Q98.4 Klinefelter syndrome, unspecified Q98.5 Karyotype 47, XYY Q98.6 Male with structurally abnormal sex chromosome Q98.7 Male with sex chromosome mosaicism Q98.8 Other specified sex chromosome abnormalities, male phenotype Q98.9 Sex chromosome abnormality, male phenotype, unspecified
Additional references
AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

Maps to no condition category in any loaded model.

Presence is a property of the code. Untick a model to hide it everywhere.

This code

Billable
yes
Code set
FY2026
Parent
Q98
Block
Q90-Q99
Siblings
8

Present FY2024–FY2027.