Q89.81

Kabuki syndrome

Billable FY2026 2025-10-01 → 2026-09-30 FY2026–2027 only

Instructional notes 4

Use additional code

Inclusion terms

Index entries leading here 1

Syndrome — see also Disease
- Kabuki (type 1, due to KMT2D mutation) (type 2, due to KDM6A mutation) Q89.81
- Niikawa-Kuroki Q89.81

Alongside this code 1 same parent — Q89.8

Additional references

AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

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Present FY2026–FY2027.