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Q85.89

Other phakomatoses, not elsewhere classified

Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 3 never code together
Q85code
Excludes1
  • ataxia telangiectasia [Louis-Bar] (G11.3)G11.3
  • familial dysautonomia [Riley-Day] (G90.1)G90.1
Q85.8code
Excludes1
  • Meckel-Gruber syndrome (Q61.9)Q61.9

Excludes1 — never code together. The excluded condition and this one are mutually exclusive.

Instructional notes 2
Q85.89code
Inclusion terms
  • Peutz-Jeghers syndrome
  • Sturge-Weber(-Dimitri) syndrome
Index entries leading here 7
  • Angiomatosis Q82.8
  • Dimitri-Sturge-Weber disease Q85.89
  • Kraft-Weber-Dimitri disease Q85.89
  • Syndrome — see also Disease
  • Peutz-Jeghers disease or syndrome Q85.89
  • Phakomatosis Q85.9
  • Sturge (-Weber) (-Dimitri) (-Kalischer) disease or syndrome Q85.89
Alongside this code 3 same parent — Q85.8
Q85.81 PTEN hamartoma tumor syndrome Q85.82 Other Cowden syndrome Q85.83 Von Hippel-Lindau syndrome
Additional references
AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

CMS22HCC12 CMS28HCC23 ESRD21HCC12 ESRD24HCC12 RX08HCC22

Presence is a property of the code. Untick a model to hide it everywhere.

This code

Billable
yes
Code set
FY2026
Parent
Q85.8
Block
Q80-Q89
Siblings
3

Present FY2024–FY2027.