Q40.0

Congenital hypertrophic pyloric stenosis

Billable FY2026 2025-10-01 → 2026-09-30

Instructional notes 5

Q40.0code

Inclusion terms

Congenital or infantile constriction
Congenital or infantile hypertrophy
Congenital or infantile spasm
Congenital or infantile stenosis
Congenital or infantile stricture

Index entries leading here 8

Achalasia (cardia) (esophagus) K22.0
- pylorus Q40.0
Stricture — see also Stenosis
- pylorus (hypertrophic) K31.1
  - congenital Q40.0
  - infantile Q40.0
Stenosis, stenotic (cicatricial) — see also Stricture
- pylorus (hypertrophic) (acquired) K31.1
  - congenital Q40.0
  - infantile Q40.0
Pylorospasm (reflex) NEC K31.3
- congenital or infantile Q40.0
- newborn Q40.0
Spasm (s) , spastic, spasticity R25.2
- pylorus NEC K31.3
  - congenital or infantile Q40.0
Obstruction, obstructed, obstructive
- pylorus
  - congenital or infantile Q40.0
Hypertrophy, hypertrophic
- pylorus (adult) (muscle) (sphincter) K31.1
  - congenital or infantile Q40.0
Constriction — see also Stricture
- pylorus (adult hypertrophic) K31.1
  - congenital or infantile Q40.0
  - newborn Q40.0

Alongside this code 5 same parent — Q40

Q40.1 Congenital hiatus hernia Q40.2 Other specified congenital malformations of stomach Q40.3 Congenital malformation of stomach, unspecified Q40.8 Oth congenital malformations of upper alimentary tract Q40.9 Congenital malformation of upper alimentary tract, unsp

Medications 1

2 Pyloric Stenosis drugs

MED-RT files conditions by MeSH, which carves the world differently from ICD-10. These are name matches on this code's description, offered as candidates — not as an assertion that they are this code.

Additional references

AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

This code

Billable: yes
Code set: FY2026
Parent: Q40
Block: Q38-Q45
Siblings: 5

Present FY2024–FY2027.

Q40.0

Risk adjustment

This code