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Q33.0

Congenital cystic lung

Billable FY2026 2025-10-01 → 2026-09-30

Exclusions 2 never code together

Excludes1

cystic fibrosis (E84.0)E84.0 E84.0
cystic lung disease, acquired or unspecified (J98.4)J98.4 J98.4

Excludes1 — never code together. The excluded condition and this one are mutually exclusive.

Instructional notes 3

Inclusion terms

Congenital cystic lung disease
Congenital honeycomb lung
Congenital polycystic lung disease

Index entries leading here 5

Cyst (colloid) (mucous) (simple) (retention)
- bronchogenic (mediastinal) (sequestration) J98.4
  - congenital Q33.0
- lung J98.4
  - congenital Q33.0
- congenital NEC Q89.89
  - lung Q33.0
Cystic — see also condition
- lung disease J98.4
  - congenital Q33.0
Disease, diseased — see also Syndrome
- cystic
  - lung J98.4
    - congenital Q33.0
- lung J98.4
  - cystic J98.4
    - congenital Q33.0
  - polycystic J98.4
    - congenital Q33.0
- polycystic
  - lung or pulmonary J98.4
    - congenital Q33.0
Honeycomb lung J98.4
- congenital Q33.0
Polycystic (disease)
- lung J98.4
  - congenital Q33.0

Alongside this code 8 same parent — Q33

Q33.1 Accessory lobe of lung Q33.2 Sequestration of lung Q33.3 Agenesis of lung Q33.4 Congenital bronchiectasis Q33.5 Ectopic tissue in lung Q33.6 Congenital hypoplasia and dysplasia of lung Q33.8 Other congenital malformations of lung Q33.9 Congenital malformation of lung, unspecified

Additional references

AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

Maps to no condition category in any loaded model.

Presence is a property of the code. Untick a model to hide it everywhere.

This code

Billable: yes
Code set: FY2026
Parent: Q33
Block: Q30-Q34
Siblings: 8

Present FY2024–FY2027.