Q25.49
Other congenital malformations of aorta
Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 1 never code together
Instructional notes 2
Q25.49code
Inclusion terms
- Aortic arch
- Bovine arch
Index entries leading here 10
- Absence (of) (organ or part) (complete or partial)
- transverse aortic arch, congenital Q25.49
- Anomaly, anomalous (congenital) (unspecified type) Q89.9
- sinus of Valsalva Q25.49
- Overriding
- aorta Q25.49
- Malformation (congenital) — see also Anomaly
- Malposition
- congenital
- aorta Q25.49
- congenital
- Arch
- Congenital — see also condition
- aortic septum Q25.49
- Deformity Q89.9
- transverse aortic arch (congenital) Q25.49
- Persistence, persistent (congenital)
- left
- root with right arch of aorta Q25.49
- left
- Pseudotruncus arteriosus Q25.49
Alongside this code 9 same parent — Q25.4
Q25.40 Congenital malformation of aorta unspecified Q25.41 Absence and aplasia of aorta Q25.42 Hypoplasia of aorta Q25.43 Congenital aneurysm of aorta Q25.44 Congenital dilation of aorta Q25.45 Double aortic arch Q25.46 Tortuous aortic arch Q25.47 Right aortic arch Q25.48 Anomalous origin of subclavian artery
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.