J43.0

Unilateral pulmonary emphysema [MacLeod's syndrome]

Billable FY2026 2025-10-01 → 2026-09-30

Exclusions 20 never code together

J43code

Excludes1

compensatory emphysema (J98.3)J98.3
interstitial emphysema (J98.2)J98.2
mediastinal emphysema (J98.2)J98.2
neonatal interstitial emphysema (P25.0)P25.0
surgical (subcutaneous) emphysema (T81.82)T81.82

Excludes2

emphysema due to inhalation of chemicals, gases, fumes or vapors (J68.4)J68.4
emphysema with chronic (obstructive) bronchitis (J44.-)J44.-
emphysematous (obstructive) bronchitis (J44.-)J44.-
traumatic subcutaneous emphysema (T79.7)T79.7

J40-J4Ablock

Excludes1

bronchitis due to chemicals, gases, fumes and vapors (J68.0)J68.0

Excludes2

cystic fibrosis (E84.-)E84.-

J00-J99chapter

Excludes2

certain conditions originating in the perinatal period (P04-P96)P04-P96
certain infectious and parasitic diseases (A00-B99)A00-B99
complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
neoplasms (C00-D49)C00-D49
smoke inhalation (T59.81-)T59.81-
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94

Excludes1 — never code together. The excluded condition and this one are mutually exclusive.

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 13

J43.0code

Inclusion terms

Swyer-James syndrome
Unilateral emphysema
Unilateral hyperlucent lung
Unilateral pulmonary artery functional hypoplasia
Unilateral transparency of lung

J00-J99chapter

Notes

When a respiratory condition is described as occurring in more than one site and is not specifically indexed, it should be classified to the lower anatomic site (e.g. tracheobronchitis to bronchitis in J40).J40

Use additional code

code, where applicable, to identify:
exposure to environmental tobacco smoke (Z77.22)Z77.22
exposure to tobacco smoke in the perinatal period (P96.81)P96.81
history of tobacco dependence (Z87.891)Z87.891
occupational exposure to environmental tobacco smoke (Z57.31)Z57.31
tobacco dependence (F17.-)F17.-
tobacco use (Z72.0)Z72.0

Index entries leading here 5

Hypoplasia, hypoplastic
- pulmonary (not associated with short gestation) Q33.6
  - artery, functional J43.0
- artery (peripheral) Q27.8
  - pulmonary Q25.79
    - functional, unilateral J43.0
Emphysema (atrophic) (bullous) (chronic) (interlobular) (lung) (obstructive) (pulmonary) (senile) (vesicular) J43.9
- unilateral J43.0
Hyperlucent lung, unilateral J43.0
MacLeod's syndrome J43.0
Transparency, lung, unilateral J43.0

Alongside this code 4 same parent — J43

J43.1 Panlobular emphysema J43.2 Centrilobular emphysema J43.8 Other emphysema J43.9 Emphysema, unspecified

Medications 1

33 Pulmonary Emphysema drugs

MED-RT files conditions by MeSH, which carves the world differently from ICD-10. These are name matches on this code's description, offered as candidates — not as an assertion that they are this code.

Additional references

AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

CMS22HCC111 · HCC112 CMS28HCC280 ESRD21HCC111 · HCC112 ESRD24HCC111 · HCC112 RX08HCC229

Presence is a property of the code. Untick a model to hide it everywhere.

This code

Billable: yes
Code set: FY2026
Parent: J43
Block: J40-J4A
Siblings: 4

Present FY2024–FY2027.