E83.822
ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
Billable FY2026 2025-10-01 → 2026-09-30
FY2026–2027 only
Exclusions 10 never code together
E83code
E70-E88block
E00-E89chapter
Excludes1
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)P70-P74
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 1
E00-E89chapter
Notes
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.E05.8E07.0E16-E31E34.-
Index entries leading here 1
- Deficiency, deficient
- ENPP1
- causing
- autosomal recessive hypophosphatemic rickets type 2 E83.822
- causing
- ENPP1
Alongside this code 5 same parent — E83.82
E83.820 Gen arterial calcifcn of infancy with unsp genetic causality E83.821 ENPP1 deficiency causing gen arterial calcifcn of infancy E83.823 ABCC6 deficiency causing gen arterial calcifcn of infancy E83.824 ABCC6 deficiency causing pseudoxanthoma elasticum E83.825 CD73 deficiency causing arterial calcification
Medications 3
4 Rickets, Hypophosphatemic drugs 4 Familial Hypophosphatemic Rickets drugs 81 Diabetes Mellitus, Type 2 drugs
MED-RT files conditions by MeSH, which carves the world differently from ICD-10. These are name matches on this code's description, offered as candidates — not as an assertion that they are this code.
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.