E83.821
ENPP1 deficiency causing generalized arterial calcification of infancy
Billable FY2026 2025-10-01 → 2026-09-30
FY2026–2027 only
Exclusions 10 never code together
E83code
E70-E88block
E00-E89chapter
Excludes1
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)P70-P74
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 4
E83.821code
E00-E89chapter
Notes
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.E05.8E07.0E16-E31E34.-
Index entries leading here 2
Alongside this code 5 same parent — E83.82
E83.820 Gen arterial calcifcn of infancy with unsp genetic causality E83.822 ENPP1 def cause autosom recess hypophosphate rickets type 2 E83.823 ABCC6 deficiency causing gen arterial calcifcn of infancy E83.824 ABCC6 deficiency causing pseudoxanthoma elasticum E83.825 CD73 deficiency causing arterial calcification
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.