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E83.01

Wilson's disease

Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 10 never code together
E83code
Excludes1
  • dietary mineral deficiency (E58-E61)E58-E61
  • parathyroid disorders (E20-E21)E20-E21
  • vitamin D deficiency (E55.-)E55.-
E70-E88block
Excludes1
  • androgen insensitivity syndrome (E34.5-)E34.5-
  • congenital adrenal hyperplasia (E25.0)E25.0
  • hemolytic anemias attributable to enzyme disorders (D55.-)D55.-
  • Marfan syndrome (Q87.4-)Q87.4-
  • 5-alpha-reductase deficiency (E29.1)E29.1
Excludes2
  • Ehlers-Danlos syndromes (Q79.6-)Q79.6-
E00-E89chapter
Excludes1
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)P70-P74

Excludes1 — never code together. The excluded condition and this one are mutually exclusive.

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 2
E83.01code
Code also
  • associated Kayser Fleischer ring (H18.04-)H18.04-
E00-E89chapter
Notes
  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.E05.8E07.0E16-E31E34.-
Index entries leading here 15
  • Syndrome — see also Disease
    • amyostatic (Wilson's disease) E83.01
    • lenticular, progressive E83.01
    • Wilson's (hepatolenticular degeneration) E83.01
    • Westphal-Strümpell E83.01
  • Deficiency, deficient
    • ceruloplasmin (Wilson) E83.01
  • Cirrhosis, cirrhotic (hepatic) (liver) K74.60
    • due to
      • hepatolenticular degeneration E83.01
      • Wilson's disease E83.01
  • Disorder (of) — see also Disease
  • Degeneration, degenerative
    • lenticular (familial) (progressive) (Wilson's) (with cirrhosis of liver) E83.01
    • Wilson's hepatolenticular E83.01
    • hepatolenticular (Wilson's) E83.01
  • Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety) F03.90
    • in (due to)
      • hepatolenticular degeneration E83.01
        • with behavioral disturbance E83.01
  • Disease, diseased — see also Syndrome
    • Wilson's (hepatolenticular degeneration) E83.01
    • Kinnier Wilson's (hepatolenticular degeneration) E83.01
    • hepatolenticular E83.01
  • Wilson's
    • disease or syndrome E83.01
    • hepatolenticular degeneration E83.01
  • Hepatolenticular degeneration E83.01
  • Pyelonephritis — see also Nephritis, tubulo-interstitial
    • in (due to)
  • Kinnier Wilson's disease (hepatolenticular degeneration) E83.01
  • Lenticular degeneration, progressive E83.01
  • Pseudosclerosis (brain)
    • of Westphal (Strümpell) E83.01
  • Strümpell-Westphal pseudosclerosis E83.01
  • Westphal-Strümpell syndrome E83.01
Alongside this code 2 same parent — E83.0
Additional references
AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

CMS28HCC50 RX08HCC42

Presence is a property of the code. Untick a model to hide it everywhere.

This code

Billable
yes
Code set
FY2026
Parent
E83.0
Block
E70-E88
Siblings
2

Present FY2024–FY2027.