E78.3
Hyperchylomicronemia
Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 8 never code together
E78code
Excludes1
- sphingolipidosis (E75.0-E75.3)E75.0-E75.3
E70-E88block
E00-E89chapter
Excludes1
- transitory endocrine and metabolic disorders specific to newborn (P70-P74)P70-P74
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 5
E78.3code
Inclusion terms
- Chylomicron retention disease
- Fredrickson's hyperlipoproteinemia, type I or V
- Hyperlipidemia, group D
- Mixed hyperglyceridemia
E00-E89chapter
Notes
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.E05.8E07.0E16-E31E34.-
Index entries leading here 14
- Syndrome — see also Disease
- Bürger-Grütz E78.3
- Bürger-Grütz disease or syndrome E78.3
- Disease, diseased — see also Syndrome
- Chylomicronemia (fasting) (with hyperprebetalipoproteinemia) E78.3
- Hyperlipemia, hyperlipidemia E78.5
- group
- D E78.3
- group
- Frederickson's hyperlipoproteinemia, type
- I and V E78.3
- Hyperlipoproteinemia E78.5
- Lipidosis E75.6
- hepatosplenomegalic E78.3
- Hepatosplenomegaly R16.2
- hyperlipemic (Bürger-Grütz type) E78.3
- Hyperchylomicronemia (familial) (primary) E78.3
- with hyperbetalipoproteinemia E78.3
- Hyperglyceridemia (endogenous) (essential) (familial) (hereditary) (pure) E78.1
- mixed E78.3
- Xanthoma (s), xanthomatosis (primary) (familial) (hereditary) E78.2
- Lipemia — see also Hyperlipidemia
- retina, retinalis E78.3
- Prebetalipoproteinemia (acquired) (essential) (familial) (hereditary) (primary) (secondary) E78.1
- with chylomicronemia E78.3
Alongside this code 9 same parent — E78
E78.0 Pure hypercholesterolemia category E78.1 Pure hyperglyceridemia E78.2 Mixed hyperlipidemia E78.4 Other hyperlipidemia category E78.5 Hyperlipidemia, unspecified E78.6 Lipoprotein deficiency E78.7 Disorders of bile acid and cholesterol metabolism category E78.8 Other disorders of lipoprotein metabolism category E78.9 Disorder of lipoprotein metabolism, unspecified
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.