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E71.313

Glutaric aciduria type II

Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 12 never code together
E71.313code
Excludes1
  • glutaric aciduria (type 1) NOS (E72.3)E72.3
E71.3code
Excludes1
  • peroxisomal disorders (E71.5)E71.5
  • Refsum's disease (G60.1)G60.1
  • Schilder's disease (G37.0)G37.0
Excludes2
  • carnitine deficiency due to inborn error of metabolism (E71.42)E71.42
E70-E88block
Excludes1
  • androgen insensitivity syndrome (E34.5-)E34.5-
  • congenital adrenal hyperplasia (E25.0)E25.0
  • hemolytic anemias attributable to enzyme disorders (D55.-)D55.-
  • Marfan syndrome (Q87.4-)Q87.4-
  • 5-alpha-reductase deficiency (E29.1)E29.1
Excludes2
  • Ehlers-Danlos syndromes (Q79.6-)Q79.6-
E00-E89chapter
Excludes1
  • transitory endocrine and metabolic disorders specific to newborn (P70-P74)P70-P74

Excludes1 — never code together. The excluded condition and this one are mutually exclusive.

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 4
E71.313code
Inclusion terms
  • Glutaric aciduria type II A
  • Glutaric aciduria type II B
  • Glutaric aciduria type II C
E00-E89chapter
Notes
  • All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.E05.8E07.0E16-E31E34.-
Index entries leading here 1
Alongside this code 5 same parent — E71.31
E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency E71.311 Medium chain acyl CoA dehydrogenase deficiency E71.312 Short chain acyl CoA dehydrogenase deficiency E71.314 Muscle carnitine palmitoyltransferase deficiency E71.318 Other disorders of fatty-acid oxidation
Additional references
AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

CMS22HCC23 ESRD21HCC23 ESRD24HCC23 RX08HCC43

Presence is a property of the code. Untick a model to hide it everywhere.

This code

Billable
yes
Code set
FY2026
Parent
E71.31
Block
E70-E88
Siblings
5

Present FY2024–FY2027.