E71.310

Long chain/very long chain acyl CoA dehydrogenase deficiency

Billable FY2026 2025-10-01 → 2026-09-30

Exclusions 11 never code together

E71.3code

Excludes1

peroxisomal disorders (E71.5)E71.5
Refsum's disease (G60.1)G60.1
Schilder's disease (G37.0)G37.0

Excludes2

carnitine deficiency due to inborn error of metabolism (E71.42)E71.42

E70-E88block

Excludes1

androgen insensitivity syndrome (E34.5-)E34.5-
congenital adrenal hyperplasia (E25.0)E25.0
hemolytic anemias attributable to enzyme disorders (D55.-)D55.-
Marfan syndrome (Q87.4-)Q87.4-
5-alpha-reductase deficiency (E29.1)E29.1

Excludes2

Ehlers-Danlos syndromes (Q79.6-)Q79.6-

E00-E89chapter

Excludes1

transitory endocrine and metabolic disorders specific to newborn (P70-P74)P70-P74

Excludes1 — never code together. The excluded condition and this one are mutually exclusive.

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 3

E71.310code

Inclusion terms

LCAD deficiency
VLCAD deficiency

E00-E89chapter

Notes

All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.E05.8 E07.0 E16-E31 E34.-

Index entries leading here 2

Deficiency, deficient
- dehydrogenase
  - long chain/very long chain acyl CoA E71.310
- LCAD (long chain acyl CoA dehydrogenase deficiency) E71.310
- VLCAD (very long chain acyl CoA dehydrogenase deficiency) E71.310
Disorder (of) — see also Disease
- fatty acid
  - oxidation
    - LCAD E71.310

Alongside this code 5 same parent — E71.31

E71.311 Medium chain acyl CoA dehydrogenase deficiency E71.312 Short chain acyl CoA dehydrogenase deficiency E71.313 Glutaric aciduria type II E71.314 Muscle carnitine palmitoyltransferase deficiency E71.318 Other disorders of fatty-acid oxidation

Medications 1

12 Glucosephosphate Dehydrogenase Deficiency drugs

MED-RT files conditions by MeSH, which carves the world differently from ICD-10. These are name matches on this code's description, offered as candidates — not as an assertion that they are this code.

Additional references

AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

CMS22HCC23 ESRD21HCC23 ESRD24HCC23 RX08HCC43

Presence is a property of the code. Untick a model to hide it everywhere.

This code

Billable: yes
Code set: FY2026
Parent: E71.31
Block: E70-E88
Siblings: 5

Present FY2024–FY2027.