D89.44
Hereditary alpha tryptasemia
Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 26 never code together
D89.4code
Excludes1
- aggressive systemic mastocytosis (C96.21)C96.21
- congenital cutaneous mastocytosis (Q82.2)Q82.2
- (non-congenital) cutaneous mastocytosis (D47.01)D47.01
- (indolent) systemic mastocytosis (D47.02)D47.02
- malignant mast cell neoplasm (C96.2-)C96.2-
- malignant mastocytoma (C96.29)C96.29
- mast cell leukemia (C94.3-)C94.3-
- mast cell sarcoma (C96.22)C96.22
- mastocytoma NOS (D47.09)D47.09
- other mast cell neoplasms of uncertain behavior (D47.09)D47.09
- systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02)D47.02
D89code
D80-D89block
D50-D89chapter
Excludes2
- autoimmune disease (systemic) NOS (M35.9)M35.9
- certain conditions originating in the perinatal period (P00-P96)P00-P96
- complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
- endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
- human immunodeficiency virus [HIV] disease (B20)B20
- injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
- neoplasms (C00-D49)C00-D49
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 6
Index entries leading here 3
Alongside this code 5 same parent — D89.4
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.