D68.2
Hereditary deficiency of other clotting factors
Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 12 never code together
D68code
D50-D89chapter
Excludes2
- autoimmune disease (systemic) NOS (M35.9)M35.9
- certain conditions originating in the perinatal period (P00-P96)P00-P96
- complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
- endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
- human immunodeficiency virus [HIV] disease (B20)B20
- injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
- neoplasms (C00-D49)C00-D49
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 13
D68.2code
Inclusion terms
- AC globulin deficiency
- Congenital afibrinogenemia
- Deficiency of factor I [fibrinogen]
- Deficiency of factor II [prothrombin]
- Deficiency of factor V [labile]
- Deficiency of factor VII [stable]
- Deficiency of factor X [Stuart-Prower]
- Deficiency of factor XII [Hageman]
- Deficiency of factor XIII [fibrin stabilizing]
- Dysfibrinogenemia (congenital)
- Hypoproconvertinemia
- Owren's disease
- Proaccelerin deficiency
Index entries leading here 17
- Absence (of) (organ or part) (complete or partial)
- fibrinogen (congenital) D68.2
- Deficiency, deficient
- accelerator globulin (Ac G) (blood) D68.2
- AC globulin (congenital) (hereditary) D68.2
- activating factor (blood) D68.2
- autoprothrombin
- coagulation NOS D68.9
- clotting factor NEC D68.2
- clotting factor NEC (hereditary) D68.2
- contact factor D68.2
- Laki-Lorand factor D68.2
- proaccelerin (congenital) (hereditary) D68.2
- proconvertin factor (congenital) (hereditary) D68.2
- prothrombin (congenital) (heredItary) D68.2
- SPCA (factor VII) D68.2
- stable factor (congenital) (hereditary) D68.2
- Stuart-Prower (factor X) D68.2
- thrombokinase D68.2
- Prower factor D68.2
- factor — see also Deficiency, coagulation
- fibrin-stabilizing factor (congenital) (hereditary) D68.2
- fibrinase D68.2
- fibrinogen (congenital) (hereditary) D68.2
- glass factor D68.2
- Hageman factor D68.2
- labile factor (congenital) (hereditary) D68.2
- Afibrinogenemia D68.8
- congenital D68.2
- Defect, defective Q89.9
- Fibrinogenopenia D68.8
- congenital D68.2
- Hypofibrinogenemia D68.8
- congenital (hereditary) D68.2
- Disease, diseased — see also Syndrome
- Dysfibrinogenemia (congenital) D68.2
- Fibrinopenia (hereditary) D68.2
- Hageman's factor defect, deficiency or disease D68.2
- Hypoproconvertinemia, congenital (hereditary) D68.2
- Hypoprothrombinemia (congenital) (hereditary) (idiopathic) D68.2
- Syndrome — see also Disease
- Owren's D68.2
- Owren's disease or syndrome (parahemophilia) D68.2
- Parahemophilia D68.2
- Stuart deficiency disease (factor X) D68.2
- Stuart-Prower factor deficiency (factor X) D68.2
Alongside this code 8 same parent — D68
D68.0 Von Willebrand disease category D68.1 Hereditary factor XI deficiency D68.3 Hemorrhagic disorder due to circulating anticoagulants category D68.4 Acquired coagulation factor deficiency D68.5 Primary thrombophilia category D68.6 Other thrombophilia category D68.8 Other specified coagulation defects D68.9 Coagulation defect, unspecified
Medications 1
MED-RT files conditions by MeSH, which carves the world differently from ICD-10. These are name matches on this code's description, offered as candidates — not as an assertion that they are this code.
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.