D61.02

Shwachman-Diamond syndrome

Billable FY2026 2025-10-01 → 2026-09-30

Exclusions 10 never code together

D61code

Excludes2

Excludes2

autoimmune disease (systemic) NOS (M35.9)M35.9
certain conditions originating in the perinatal period (P00-P96)P00-P96
complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
human immunodeficiency virus [HIV] disease (B20)B20
injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
neoplasms (C00-D49)C00-D49
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 5

Use additional code

code, if applicable, for genetic susceptibility to other malignant neoplasm (Z15.09)Z15.09

Code also

Index entries leading here 1

Syndrome — see also Disease
- Schwachman (-Diamond) D61.02
- Shwachman (-Diamond) D61.02

Alongside this code 3 same parent — D61.0

Additional references

AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

CMS22HCC46 CMS28HCC109 ESRD21HCC46 ESRD24HCC46 RX08HCC96

Presence is a property of the code. Untick a model to hide it everywhere.

Present FY2024–FY2027.