D58.0
Hereditary spherocytosis
Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 10 never code together
D50-D89chapter
Excludes2
- autoimmune disease (systemic) NOS (M35.9)M35.9
- certain conditions originating in the perinatal period (P00-P96)P00-P96
- complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
- endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
- human immunodeficiency virus [HIV] disease (B20)B20
- injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
- neoplasms (C00-D49)C00-D49
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 3
D58.0code
Inclusion terms
- Acholuric (familial) jaundice
- Congenital (spherocytic) hemolytic icterus
- Minkowski-Chauffard syndrome
Index entries leading here 5
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) D64.9
- Disease, diseased — see also Syndrome
- hemoglobin or Hb
- spherocytosis D58.0
- hemoglobin or Hb
- Spherocytosis (congenital) (familial) (hereditary) D58.0
- hemoglobin disease D58.0
- Jaundice (yellow) R17
- Syndrome — see also Disease
- Minkowski-Chauffard D58.0
Alongside this code 4 same parent — D58
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.