Q14.1
Congenital malformation of retina
Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 8 never code together
Q10-Q18block
Excludes2
- cleft lip and cleft palate (Q35-Q37)Q35-Q37
- congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)Q05.0Q05.5Q67.5Q76.0-Q76.4
- congenital malformation of larynx (Q31.-)Q31.-
- congenital malformation of lip NEC (Q38.0)Q38.0
- congenital malformation of nose (Q30.-)Q30.-
- congenital malformation of parathyroid gland (Q89.2)Q89.2
- congenital malformation of thyroid gland (Q89.2)Q89.2
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 1
Q14.1code
Inclusion terms
- Congenital retinal aneurysm
Index entries leading here 14
- Aberrant (congenital) — see also Malposition, congenital
- Aneurysm (anastomotic) (artery) (cirsoid) (diffuse) (false) (fusiform) (multiple) (saccular) I72.9
- Anomaly, anomalous (congenital) (unspecified type) Q89.9
- Aplasia — see also Agenesis
- fovea centralis (congenital) Q14.1
- Stricture — see also Stenosis
- Hypoplasia, hypoplastic
- Imperfect
- closure (congenital)
- retina Q14.1
- closure (congenital)
- Retinoschisis H33.10
- congenital Q14.1
- Displacement, displaced
- macula (congenital) Q14.1
- Dysplasia — see also Anomaly
- retinal, congenital Q14.1
- Malformation (congenital) — see also Anomaly
- retina Q14.1
- Medullated fibers
- retina Q14.1
- Pigmentation (abnormal) (anomaly) L81.9
- retina, congenital (grouped) (nevoid) Q14.1
- Tortuous
- retinal vessel, congenital Q14.1
Alongside this code 5 same parent — Q14
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.