K00.5
Hereditary disturbances in tooth structure, not elsewhere classified
Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 9 never code together
K00-K95chapter
Excludes2
- certain conditions originating in the perinatal period (P04-P96)P04-P96
- certain infectious and parasitic diseases (A00-B99)A00-B99
- complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
- endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
- injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
- neoplasms (C00-D49)C00-D49
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 5
K00.5code
Inclusion terms
- Amelogenesis imperfecta
- Dentinogenesis imperfecta
- Odontogenesis imperfecta
- Dentinal dysplasia
- Shell teeth
Index entries leading here 10
- Amelogenesis imperfecta K00.5
- Brown enamel of teeth (hereditary) K00.5
- Defect, defective Q89.9
- dentin (hereditary) K00.5
- Dentin
- opalescent K00.5
- Dysplasia — see also Anomaly
- dentinal K00.5
- Dentinogenesis imperfecta K00.5
- Disturbance (s) — see also Disease
- tooth
- structure, hereditary NEC K00.5
- tooth
- Odontogenesis imperfecta K00.5
- Opalescent dentin (hereditary) K00.5
- Shell teeth K00.5
Alongside this code 9 same parent — K00
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.