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D80.0

Hereditary hypogammaglobulinemia

Billable FY2026 2025-10-01 → 2026-09-30
Exclusions 12 never code together
D80-D89block
Excludes1
  • autoimmune disease (systemic) NOS (M35.9)M35.9
  • functional disorders of polymorphonuclear neutrophils (D71-)D71-
  • human immunodeficiency virus [HIV] disease (B20)B20
D50-D89chapter
Excludes2
  • autoimmune disease (systemic) NOS (M35.9)M35.9
  • certain conditions originating in the perinatal period (P00-P96)P00-P96
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
  • endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
  • human immunodeficiency virus [HIV] disease (B20)B20
  • injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
  • neoplasms (C00-D49)C00-D49
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94

Excludes1 — never code together. The excluded condition and this one are mutually exclusive.

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 5
D80.0code
Inclusion terms
  • Autosomal recessive agammaglobulinemia (Swiss type)
  • X-linked agammaglobulinemia [Bruton] (with growth hormone deficiency)
D80-D89block
Includes
  • defects in the complement system
  • immunodeficiency disorders, except human immunodeficiency virus [HIV] disease
  • sarcoidosis
Index entries leading here 7
  • Absence (of) (organ or part) (complete or partial)
  • Agammaglobulinemia (acquired (secondary)) (nonfamilial) D80.1
    • autosomal recessive (Swiss type) D80.0
    • Bruton's X-linked D80.0
    • congenital sex-linked D80.0
    • Swiss type (autosomal recessive) D80.0
    • X-linked (with growth hormone deficiency) (Bruton) D80.0
    • hereditary D80.0
  • Syndrome — see also Disease
  • Immunodeficiency D84.9
    • autosomal recessive, Swiss type D80.0
  • Bruton's X-linked agammaglobulinemia D80.0
  • Deficiency, deficient
  • Hypogammaglobulinemia D80.1
Alongside this code 9 same parent — D80
D80.1 Nonfamilial hypogammaglobulinemia D80.2 Selective deficiency of immunoglobulin A [IgA] D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses D80.4 Selective deficiency of immunoglobulin M [IgM] D80.5 Immunodeficiency with increased immunoglobulin M [IgM] D80.6 Antibody defic w near-norm immunoglob or w hyperimmunoglob D80.7 Transient hypogammaglobulinemia of infancy D80.8 Other immunodeficiencies with predominantly antibody defects D80.9 Immunodeficiency with predominantly antibody defects, unsp
Additional references
AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

Risk adjustment

CMS22HCC47 CMS28HCC115 ESRD21HCC47 ESRD24HCC47 RX08HCC99

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This code

Billable
yes
Code set
FY2026
Parent
D80
Block
D80-D89
Siblings
9

Present FY2024–FY2027.