D56.0

Alpha thalassemia

Billable FY2026 2025-10-01 → 2026-09-30

Exclusions 14 never code together

Excludes1

D56code

Excludes1

Excludes2

autoimmune disease (systemic) NOS (M35.9)M35.9
certain conditions originating in the perinatal period (P00-P96)P00-P96
complications of pregnancy, childbirth and the puerperium (O00-O9A)O00-O9A
congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)Q00-Q99
endocrine, nutritional and metabolic diseases (E00-E88)E00-E88
human immunodeficiency virus [HIV] disease (B20)B20
injury, poisoning and certain other consequences of external causes (S00-T88)S00-T88
neoplasms (C00-D49)C00-D49
symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)R00-R94

Excludes1 — never code together. The excluded condition and this one are mutually exclusive.

Excludes2 — not included here, but the patient may have both. Code both when documented.

Instructional notes 7

Inclusion terms

Use additional code

code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)P56.99 P56.99

Index entries leading here 5

Thalassemia (anemia) (disease) D56.9
- alpha (major) (severe) (triple gene defect) D56.0
Hydrops R60.9
- fetalis P83.2
  - due to
    - alpha thalassemia D56.0
- newborn (idiopathic) P83.2
  - due to
    - alpha thalassemia D56.0
Disease, diseased — see also Syndrome
- hemoglobin or Hb
  - Bart's D56.0
  - H (Hb-H) (thalassemia) D56.0
    - Constant Spring D56.0
Hb (abnormal)
- Bart's disease D56.0
Hemoglobin — see also condition
- H Constant Spring D56.0

Alongside this code 7 same parent — D56

Additional references

AHA Coding Clinic® Licence required

Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.

CMS22HCC48 ESRD21HCC48 ESRD24HCC48

Presence is a property of the code. Untick a model to hide it everywhere.

Present FY2024–FY2027.