A81.00
Creutzfeldt-Jakob disease, unspecified
Billable FY2026 2025-10-01 → 2026-09-30
This is the unspecified option. 2 more
specific codes sit alongside it. Worth
checking whether the documentation supports one of them.
Exclusions 8 never code together
A80-A89block
A00-B99chapter
Excludes1
- certain localized infections - see body system-related chapters
Excludes2
- carrier or suspected carrier of infectious disease (Z22.-)Z22.-
- infectious and parasitic diseases complicating pregnancy, childbirth and the puerperium (O98.-)O98.-
- infectious and parasitic diseases specific to the perinatal period (P35-P39)P35-P39
- influenza and other acute respiratory infections (J00-J22)J00-J22
Excludes1 — never code together. The excluded condition and this one are mutually exclusive.
Excludes2 — not included here, but the patient may have both. Code both when documented.
Instructional notes 11
A81code
Includes
- diseases of the central nervous system caused by prions
Use additional code
- code, if applicable, to identify:
- dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)F02.84F02.A4F02.B4F02.C4
- dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)F02.81-F02.A1-F02.B1-F02.C1-
- dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)F02.83F02.A3F02.B3F02.C3
- dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)F02.82F02.A2F02.B2F02.C2
- dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)F02.80F02.A0F02.B0F02.C0
- mild neurocognitive disorder due to known physiological condition (F06.7-)F06.7-
A81.00code
Inclusion terms
- Jakob-Creutzfeldt disease, unspecified
Index entries leading here 2
Alongside this code 2 same parent — A81.0
Additional references
AHA Coding Clinic® Licence required
Official coding advice for this code. Published by the American Hospital Association. Not included in this installation.